Congenital lymphangiomatosis: Multidisciplinary approach
Background: Diffuse lymphangiomatosis is a rare disorder of the lymphatic vessels. Its prognosis is poor and its treatment not codified. Methods: We describe the case of a 14 years old boy known for a lymphatic malformation of the left chest wall with pleuropulmonary, bone and visceral involvement....
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2020-10-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576620302554 |
| _version_ | 1818341438295900160 |
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| author | Oumama El Ezzi Guillaume Saliou Carole Gengler Anthony de Buys Roessingh |
| author_facet | Oumama El Ezzi Guillaume Saliou Carole Gengler Anthony de Buys Roessingh |
| author_sort | Oumama El Ezzi |
| collection | DOAJ |
| description | Background: Diffuse lymphangiomatosis is a rare disorder of the lymphatic vessels. Its prognosis is poor and its treatment not codified. Methods: We describe the case of a 14 years old boy known for a lymphatic malformation of the left chest wall with pleuropulmonary, bone and visceral involvement. He presented with respiratory difficulties and a left pleural effusion. The treatment associated thoracic drainage, surgical pleurectomy and iterative sclerotherapy. Results: The patient is currently asymptomatic. On imaging, there is a decrease of the left lateral thoracic component and a resolution of the intra-pleural portion. Conclusions: The treatment of diffuse lymphangiomatosis is based on a multimodal management. |
| first_indexed | 2024-12-13T15:58:48Z |
| format | Article |
| id | doaj.art-f86d0a662f474624938a2dc605a7083e |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-12-13T15:58:48Z |
| publishDate | 2020-10-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-f86d0a662f474624938a2dc605a7083e2022-12-21T23:39:13ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662020-10-0161101621Congenital lymphangiomatosis: Multidisciplinary approachOumama El Ezzi0Guillaume Saliou1Carole Gengler2Anthony de Buys Roessingh3Service of Pediatric Surgery, University Hospital Center of the Canton of Vaud (CHUV), CH-1011, Lausanne, Switzerland; Corresponding author. Department of Pediatric Surgery, SCEA, Centre Hospitalier Universitaire Vaudois (CHUV), CH-1011, Lausanne, Switzerland.Service of Interventional Radiology, University Hospital Center of the Canton of Vaud (CHUV), CH-1011, Lausanne, SwitzerlandPathology Department, University Hospital Center of the Canton of Vaud (CHUV), CH-1011, Lausanne, SwitzerlandService of Pediatric Surgery, University Hospital Center of the Canton of Vaud (CHUV), CH-1011, Lausanne, SwitzerlandBackground: Diffuse lymphangiomatosis is a rare disorder of the lymphatic vessels. Its prognosis is poor and its treatment not codified. Methods: We describe the case of a 14 years old boy known for a lymphatic malformation of the left chest wall with pleuropulmonary, bone and visceral involvement. He presented with respiratory difficulties and a left pleural effusion. The treatment associated thoracic drainage, surgical pleurectomy and iterative sclerotherapy. Results: The patient is currently asymptomatic. On imaging, there is a decrease of the left lateral thoracic component and a resolution of the intra-pleural portion. Conclusions: The treatment of diffuse lymphangiomatosis is based on a multimodal management.http://www.sciencedirect.com/science/article/pii/S2213576620302554LymphangiomatosisSclerotherapyCongenitalPediatricsVascular malformations |
| spellingShingle | Oumama El Ezzi Guillaume Saliou Carole Gengler Anthony de Buys Roessingh Congenital lymphangiomatosis: Multidisciplinary approach Journal of Pediatric Surgery Case Reports Lymphangiomatosis Sclerotherapy Congenital Pediatrics Vascular malformations |
| title | Congenital lymphangiomatosis: Multidisciplinary approach |
| title_full | Congenital lymphangiomatosis: Multidisciplinary approach |
| title_fullStr | Congenital lymphangiomatosis: Multidisciplinary approach |
| title_full_unstemmed | Congenital lymphangiomatosis: Multidisciplinary approach |
| title_short | Congenital lymphangiomatosis: Multidisciplinary approach |
| title_sort | congenital lymphangiomatosis multidisciplinary approach |
| topic | Lymphangiomatosis Sclerotherapy Congenital Pediatrics Vascular malformations |
| url | http://www.sciencedirect.com/science/article/pii/S2213576620302554 |
| work_keys_str_mv | AT oumamaelezzi congenitallymphangiomatosismultidisciplinaryapproach AT guillaumesaliou congenitallymphangiomatosismultidisciplinaryapproach AT carolegengler congenitallymphangiomatosismultidisciplinaryapproach AT anthonydebuysroessingh congenitallymphangiomatosismultidisciplinaryapproach |