Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old Boy
Ascites is not a usual finding in prehepatic portal hypertension, including portal vein thrombosis, but when portal vein thrombosis is acute and massive, ascites can be a presenting feature. We report a 9-year-old boy with tense ascites and portal and superior mesenteric vein thrombosis. A 9-year-ol...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Tehran University of Medical Sciences
2019-07-01
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| Series: | Case Reports in Clinical Practice |
| Subjects: | |
| Online Access: | https://crcp.tums.ac.ir/index.php/crcp/article/view/220 |
| _version_ | 1818936239536996352 |
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| author | Masoumeh Asgarshirazi Mehrnoush Ghafarypour Yahya Aghighi Seyyedreza Raeeskarami Mehri Najafi |
| author_facet | Masoumeh Asgarshirazi Mehrnoush Ghafarypour Yahya Aghighi Seyyedreza Raeeskarami Mehri Najafi |
| author_sort | Masoumeh Asgarshirazi |
| collection | DOAJ |
| description | Ascites is not a usual finding in prehepatic portal hypertension, including portal vein thrombosis, but when portal vein thrombosis is acute and massive, ascites can be a presenting feature. We report a 9-year-old boy with tense ascites and portal and superior mesenteric vein thrombosis. A 9-year-old boy was evaluated for tense ascites which led to umbilical hernia since one month before admission. He did not have any clinical or laboratory stigmata of parenchymal liver disease. Imaging studies showed superior mesenteric and portal vein thrombosis. In laboratory tests for pre-thrombotic states, he suffered from significant protein S deficiency. Thrombophilic states like protein S deficiency predispose patient to vascular thrombosis. This vascular thrombosis can be present with signs and symptoms related to their territories. Prevention of thrombosis and rethrombosis with anticoagulant therapy is recommended. |
| first_indexed | 2024-12-20T05:32:54Z |
| format | Article |
| id | doaj.art-f8b26d730c79412e8bb29fe3df2a0354 |
| institution | Directory Open Access Journal |
| issn | 2538-2683 2538-2691 |
| language | English |
| last_indexed | 2024-12-20T05:32:54Z |
| publishDate | 2019-07-01 |
| publisher | Tehran University of Medical Sciences |
| record_format | Article |
| series | Case Reports in Clinical Practice |
| spelling | doaj.art-f8b26d730c79412e8bb29fe3df2a03542022-12-21T19:51:42ZengTehran University of Medical SciencesCase Reports in Clinical Practice2538-26832538-26912019-07-014110.18502/crcp.v4i1.1299Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old BoyMasoumeh Asgarshirazi0Mehrnoush Ghafarypour1Yahya Aghighi2Seyyedreza Raeeskarami3Mehri Najafi4Department of Pediatrics, School of Medicine, Tehran University of Medical Sciences, Tehran, IranDepartment of Pediatrics, School of Medicine, Tehran University of Medical Sciences, Tehran, IranDepartment of Pediatrics, School of Medicine, Tehran University of Medical Sciences, Tehran, IranDepartment of Pediatrics, School of Medicine, Tehran University of Medical Sciences, Tehran, IranDepartment of Pediatrics, School of Medicine, Tehran University of Medical Sciences, Tehran, IranAscites is not a usual finding in prehepatic portal hypertension, including portal vein thrombosis, but when portal vein thrombosis is acute and massive, ascites can be a presenting feature. We report a 9-year-old boy with tense ascites and portal and superior mesenteric vein thrombosis. A 9-year-old boy was evaluated for tense ascites which led to umbilical hernia since one month before admission. He did not have any clinical or laboratory stigmata of parenchymal liver disease. Imaging studies showed superior mesenteric and portal vein thrombosis. In laboratory tests for pre-thrombotic states, he suffered from significant protein S deficiency. Thrombophilic states like protein S deficiency predispose patient to vascular thrombosis. This vascular thrombosis can be present with signs and symptoms related to their territories. Prevention of thrombosis and rethrombosis with anticoagulant therapy is recommended.https://crcp.tums.ac.ir/index.php/crcp/article/view/220Protein S deficiencyPortal vein thrombosisAscites |
| spellingShingle | Masoumeh Asgarshirazi Mehrnoush Ghafarypour Yahya Aghighi Seyyedreza Raeeskarami Mehri Najafi Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old Boy Case Reports in Clinical Practice Protein S deficiency Portal vein thrombosis Ascites |
| title | Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old Boy |
| title_full | Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old Boy |
| title_fullStr | Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old Boy |
| title_full_unstemmed | Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old Boy |
| title_short | Tense Ascites as a Presentaton of Protein S Defciency in a 9-Year-Old Boy |
| title_sort | tense ascites as a presentaton of protein s defciency in a 9 year old boy |
| topic | Protein S deficiency Portal vein thrombosis Ascites |
| url | https://crcp.tums.ac.ir/index.php/crcp/article/view/220 |
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