Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case Reports
Pulmonary Lymphangioleiomyomatosis (LAM) is a rare disease, mostly seen in women of reproductive age group. Most common presentation is dyspnoea on exertion, may be associated with haemoptysis and chest pain. LAM is a cystic lung disease, with a poor prognosis and is difficult to treat. In this ca...
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| Format: | Article |
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JCDR Research and Publications Private Limited
2021-03-01
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| Series: | Journal of Clinical and Diagnostic Research |
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| Online Access: | https://www.jcdr.net/articles/PDF/14759/47655_CE[Ra]_F(Sh)_PF1(SK1_KM)_PFA(KM)_PB(HJ_Pr_KM)_PN(KM).pdf |
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| author | KUSUM V SHAH SONAL GOYAL SAKET KUMAR ARTI D SHAH YASH RANA |
| author_facet | KUSUM V SHAH SONAL GOYAL SAKET KUMAR ARTI D SHAH YASH RANA |
| author_sort | KUSUM V SHAH |
| collection | DOAJ |
| description | Pulmonary Lymphangioleiomyomatosis (LAM) is a rare disease, mostly seen in women of reproductive age group. Most common
presentation is dyspnoea on exertion, may be associated with haemoptysis and chest pain. LAM is a cystic lung disease, with a
poor prognosis and is difficult to treat. In this case report, two patients are discussed who presented with dyspnoea and chest pain
due to pneumothorax and were later diagnosed as case of LAM on clinical and radiological basis. Intercostal Chest Tube Drainage
(ICD) was inserted for resolution of pneumothorax and subsequently pleurodesis was done to prevent recurrent pneumothorax. In
case of recurrent pneumothorax, LAM should be considered as a differential diagnosis. Pleurodesis can be considered to prevent
recurrent pneumothorax. |
| first_indexed | 2024-12-19T10:52:34Z |
| format | Article |
| id | doaj.art-f90f049e12714829b4660dd906b62a54 |
| institution | Directory Open Access Journal |
| issn | 2249-782X 0973-709X |
| language | English |
| last_indexed | 2024-12-19T10:52:34Z |
| publishDate | 2021-03-01 |
| publisher | JCDR Research and Publications Private Limited |
| record_format | Article |
| series | Journal of Clinical and Diagnostic Research |
| spelling | doaj.art-f90f049e12714829b4660dd906b62a542022-12-21T20:24:57ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2021-03-01153OD09OD1110.7860/JCDR/2021/47655.14759Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case ReportsKUSUM V SHAH0SONAL GOYAL1 SAKET KUMAR2 ARTI D SHAH3YASH RANA4Professor, Department of Respiratory Medicine, Smt. B.K. Shah Medical Institute and Research Centre, Sumandeep Vidyapeeth Deemed to be University, Vadodara, Gujarat, India.Second Year PG Resident, Department of Respiratory Medicine, Smt. B.K. Shah Medical Institute and Research Centre, Sumandeep Vidyapeeth Deemed to be University, Vadodara, Gujarat, India.Third Year PG Resident, Department of Respiratory Medicine, Smt. B.K. Shah Medical Institute and Research Centre, Sumandeep Vidyapeeth Deemed to be University, Vadodara, Gujarat, India.Professor and Head, Department of Respiratory Medicine, Smt. B.K. Shah Medical Institute and Research Centre, Sumandeep Vidyapeeth Deemed to be University, Vadodara, Gujarat, India.Assistant Professor, Department of Respiratory Medicine, Smt. B.K. Shah Medical Institute and Research Centre, Sumandeep Vidyapeeth Deemed to be University, Vadodara, Gujarat, India.Pulmonary Lymphangioleiomyomatosis (LAM) is a rare disease, mostly seen in women of reproductive age group. Most common presentation is dyspnoea on exertion, may be associated with haemoptysis and chest pain. LAM is a cystic lung disease, with a poor prognosis and is difficult to treat. In this case report, two patients are discussed who presented with dyspnoea and chest pain due to pneumothorax and were later diagnosed as case of LAM on clinical and radiological basis. Intercostal Chest Tube Drainage (ICD) was inserted for resolution of pneumothorax and subsequently pleurodesis was done to prevent recurrent pneumothorax. In case of recurrent pneumothorax, LAM should be considered as a differential diagnosis. Pleurodesis can be considered to prevent recurrent pneumothorax.https://www.jcdr.net/articles/PDF/14759/47655_CE[Ra]_F(Sh)_PF1(SK1_KM)_PFA(KM)_PB(HJ_Pr_KM)_PN(KM).pdfcystic lung diseaseintercostal chest tube drainagerecurrent pneumothoraxreproductive age women |
| spellingShingle | KUSUM V SHAH SONAL GOYAL SAKET KUMAR ARTI D SHAH YASH RANA Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case Reports Journal of Clinical and Diagnostic Research cystic lung disease intercostal chest tube drainage recurrent pneumothorax reproductive age women |
| title | Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case Reports |
| title_full | Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case Reports |
| title_fullStr | Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case Reports |
| title_full_unstemmed | Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case Reports |
| title_short | Pulmonary Lymphangioleiomyomatosis and Role of Pleurodesis: Rare Case Reports |
| title_sort | pulmonary lymphangioleiomyomatosis and role of pleurodesis rare case reports |
| topic | cystic lung disease intercostal chest tube drainage recurrent pneumothorax reproductive age women |
| url | https://www.jcdr.net/articles/PDF/14759/47655_CE[Ra]_F(Sh)_PF1(SK1_KM)_PFA(KM)_PB(HJ_Pr_KM)_PN(KM).pdf |
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