A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary Window
Aortopulmonary window is a rare congenital anomaly which is commonly associated with other lesions such as patent ductus arteriosus, interrupted aortic arch, Atrial Septal Defect (ASD), and Ventricular Septal Defect (VSD). Aortic aneurysm and dissection have not been reported as an associated anoma...
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| Format: | Article |
| Language: | English |
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Tehran University of Medical Sciences
2023-01-01
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| Series: | Case Reports in Clinical Practice |
| Subjects: | |
| Online Access: | https://crcp.tums.ac.ir/index.php/crcp/article/view/654 |
| _version_ | 1797943824120545280 |
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| author | Ahmad Amin Mozhgan Parsaee Homa Ghaderian Fatemeh Zohrian Arezoo Mohamadifar |
| author_facet | Ahmad Amin Mozhgan Parsaee Homa Ghaderian Fatemeh Zohrian Arezoo Mohamadifar |
| author_sort | Ahmad Amin |
| collection | DOAJ |
| description |
Aortopulmonary window is a rare congenital anomaly which is commonly associated with other lesions such as patent ductus arteriosus, interrupted aortic arch, Atrial Septal Defect (ASD), and Ventricular Septal Defect (VSD). Aortic aneurysm and dissection have not been reported as an associated anomaly in AP window.A 44 -year-old male, with inoperable AortoPulmonary Window (AP window) and Eisenmenger syndrome presented to our Emergency Department with back pain and shortness of breath. Transthoracic echocardiography and aortic CT angiography depicted aneurysmal dilatation of ascending aorta with a dissection flap which was extended to main pulmonary artery. Any intervention was very high risk, due to the risk of imminent RV failure. The patient was hemodynamically stable and the symptoms seemed to be chronic, so we decided to manage him medically.AP window is a rare congenital anomaly which is commonly associated with other anomalies. In this report, we represent a rare case of AP window and Eisenmenger syndrome with aortic aneurysm and dissecting flap in ascending aorta and pulmonary artery who was managed medically.
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| first_indexed | 2024-04-10T20:30:13Z |
| format | Article |
| id | doaj.art-f9730201bd464a889e2d9ec66adcee8a |
| institution | Directory Open Access Journal |
| issn | 2538-2683 2538-2691 |
| language | English |
| last_indexed | 2024-04-10T20:30:13Z |
| publishDate | 2023-01-01 |
| publisher | Tehran University of Medical Sciences |
| record_format | Article |
| series | Case Reports in Clinical Practice |
| spelling | doaj.art-f9730201bd464a889e2d9ec66adcee8a2023-01-25T07:34:58ZengTehran University of Medical SciencesCase Reports in Clinical Practice2538-26832538-26912023-01-017410.18502/crcp.v7i4.11599A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary WindowAhmad Amin0Mozhgan Parsaee1Homa Ghaderian2Fatemeh Zohrian3Arezoo Mohamadifar4Department of Heart Failure and Transplantation, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.Echocardiography Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, IranTehran Heart Center, Tehran University of Medical Sciences, Tehran, Iran.Alborz University of Medical Sciences, Karaj, Alborz, Iran.Chronic Respiratory Diseases Research Center, National Research Institute of Tuberculosis and Lung Diseases (NRITLD), Massih Daneshvari Educational and Medical Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Aortopulmonary window is a rare congenital anomaly which is commonly associated with other lesions such as patent ductus arteriosus, interrupted aortic arch, Atrial Septal Defect (ASD), and Ventricular Septal Defect (VSD). Aortic aneurysm and dissection have not been reported as an associated anomaly in AP window.A 44 -year-old male, with inoperable AortoPulmonary Window (AP window) and Eisenmenger syndrome presented to our Emergency Department with back pain and shortness of breath. Transthoracic echocardiography and aortic CT angiography depicted aneurysmal dilatation of ascending aorta with a dissection flap which was extended to main pulmonary artery. Any intervention was very high risk, due to the risk of imminent RV failure. The patient was hemodynamically stable and the symptoms seemed to be chronic, so we decided to manage him medically.AP window is a rare congenital anomaly which is commonly associated with other anomalies. In this report, we represent a rare case of AP window and Eisenmenger syndrome with aortic aneurysm and dissecting flap in ascending aorta and pulmonary artery who was managed medically. https://crcp.tums.ac.ir/index.php/crcp/article/view/654Aortopulmonary windowDissectionCongenital heart disease |
| spellingShingle | Ahmad Amin Mozhgan Parsaee Homa Ghaderian Fatemeh Zohrian Arezoo Mohamadifar A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary Window Case Reports in Clinical Practice Aortopulmonary window Dissection Congenital heart disease |
| title | A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary Window |
| title_full | A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary Window |
| title_fullStr | A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary Window |
| title_full_unstemmed | A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary Window |
| title_short | A Rare Case with Dissection of Pulmonary and Aorta in Aortopulmonary Window |
| title_sort | rare case with dissection of pulmonary and aorta in aortopulmonary window |
| topic | Aortopulmonary window Dissection Congenital heart disease |
| url | https://crcp.tums.ac.ir/index.php/crcp/article/view/654 |
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