Congenital Absence of the Portal Vein as a Rare Cause of Portopulmonary Hypertension—A Case Study Series
<i>Background</i>. Congenital absence of the portal vein (CAPV) is an extremely rare malformation that is caused by aberrant venous development during embryogenesis and is usually associated with congenital portosystemic shunts (CPSS). This hemodynamic allows mesenteric blood to bypass t...
Main Authors: | Tereza Hlavata, Monika Kaldararova, Filip Klauco, Erika Drangova, Adriana Reptova, Iveta Simkova |
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Format: | Article |
Language: | English |
Published: |
MDPI AG
2022-10-01
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Series: | Medicina |
Subjects: | |
Online Access: | https://www.mdpi.com/1648-9144/58/10/1484 |
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