Congenital Absence of the Portal Vein as a Rare Cause of Portopulmonary Hypertension—A Case Study Series

<i>Background</i>. Congenital absence of the portal vein (CAPV) is an extremely rare malformation that is caused by aberrant venous development during embryogenesis and is usually associated with congenital portosystemic shunts (CPSS). This hemodynamic allows mesenteric blood to bypass t...

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Bibliographic Details
Main Authors: Tereza Hlavata, Monika Kaldararova, Filip Klauco, Erika Drangova, Adriana Reptova, Iveta Simkova
Format: Article
Language:English
Published: MDPI AG 2022-10-01
Series:Medicina
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Online Access:https://www.mdpi.com/1648-9144/58/10/1484

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