Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma
Opsoclonus-ataxia, also called “dancing eye syndrome,” is a serious neurologic condition that is often a paraneoplastic manifestation of occult neuroblastoma in early childhood. Although survival is high with anti-tumoral treatment and immunosuppressive therapy, outcome generally includes significan...
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Format: | Article |
Language: | Spanish |
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Universidad Complutense de Madrid
2012-01-01
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Series: | Psicooncologia |
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Online Access: | http://revistas.ucm.es/index.php/PSIC/article/view/37889 |
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author | Águeda Sapiña Adela Cañete Tina Barahona María Plasencia María Moran Olivia Prades Davinia Fernandez Laura Arjona Paula Rubio Jordi Bernabeu |
author_facet | Águeda Sapiña Adela Cañete Tina Barahona María Plasencia María Moran Olivia Prades Davinia Fernandez Laura Arjona Paula Rubio Jordi Bernabeu |
author_sort | Águeda Sapiña |
collection | DOAJ |
description | Opsoclonus-ataxia, also called “dancing eye syndrome,” is a serious neurologic condition that is often a paraneoplastic manifestation of occult neuroblastoma in early childhood. Although survival is high with anti-tumoral treatment and immunosuppressive therapy, outcome generally includes significant developmental and behavioral sequelae. We report a case diagnosed at nine month of age, treated in our Unit and refered for a multidisciplinary neuropsychological rehabilitation when she was 4 year old. |
first_indexed | 2024-12-15T00:43:03Z |
format | Article |
id | doaj.art-f9c62c13bb9949b99f8dad8952dcaeef |
institution | Directory Open Access Journal |
issn | 1696-7240 1988-8287 |
language | Spanish |
last_indexed | 2024-12-15T00:43:03Z |
publishDate | 2012-01-01 |
publisher | Universidad Complutense de Madrid |
record_format | Article |
series | Psicooncologia |
spelling | doaj.art-f9c62c13bb9949b99f8dad8952dcaeef2022-12-21T22:41:37ZspaUniversidad Complutense de MadridPsicooncologia1696-72401988-82872012-01-0182-340542110.5209/rev_PSIC.2011.v8.n2-3.3788937733Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastomaÁgueda Sapiña0Adela Cañete1Tina Barahona2María Plasencia3María Moran4Olivia Prades5Davinia Fernandez6Laura Arjona7Paula Rubio8Jordi Bernabeu9Unidad de Daño Cerebral. Hermanas Hospitalarias, Valencia Oncología pediátrica. Hospital Universitario y Politécnico La Fe, ValenciaOncología pediátrica. Hospital Universitario y Politécnico La Fe, ValenciaOncología pediátrica. Hospital Universitario y Politécnico La Fe, Valencia Junta Asociada de Valencia de la Asociación Española Contra el Cancer.Unidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, Valencia Oncología pediátrica. Hospital Universitario y Politécnico La Fe, ValenciaOpsoclonus-ataxia, also called “dancing eye syndrome,” is a serious neurologic condition that is often a paraneoplastic manifestation of occult neuroblastoma in early childhood. Although survival is high with anti-tumoral treatment and immunosuppressive therapy, outcome generally includes significant developmental and behavioral sequelae. We report a case diagnosed at nine month of age, treated in our Unit and refered for a multidisciplinary neuropsychological rehabilitation when she was 4 year old.http://revistas.ucm.es/index.php/PSIC/article/view/37889Síndrome oposlonus-mioclonusataxianeuroblastomalate efectsneuropsicología pediátrica, síndrome paraneoplásico. |
spellingShingle | Águeda Sapiña Adela Cañete Tina Barahona María Plasencia María Moran Olivia Prades Davinia Fernandez Laura Arjona Paula Rubio Jordi Bernabeu Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma Psicooncologia Síndrome oposlonus-mioclonus ataxia neuroblastoma late efects neuropsicología pediátrica, síndrome paraneoplásico. |
title | Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma |
title_full | Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma |
title_fullStr | Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma |
title_full_unstemmed | Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma |
title_short | Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma |
title_sort | case report opsoclonus myoclonus syndrome associated with abdominal neuroblastoma |
topic | Síndrome oposlonus-mioclonus ataxia neuroblastoma late efects neuropsicología pediátrica, síndrome paraneoplásico. |
url | http://revistas.ucm.es/index.php/PSIC/article/view/37889 |
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