Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma

Opsoclonus-ataxia, also called “dancing eye syndrome,” is a serious neurologic condition that is often a paraneoplastic manifestation of occult neuroblastoma in early childhood. Although survival is high with anti-tumoral treatment and immunosuppressive therapy, outcome generally includes significan...

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Main Authors: Águeda Sapiña, Adela Cañete, Tina Barahona, María Plasencia, María Moran, Olivia Prades, Davinia Fernandez, Laura Arjona, Paula Rubio, Jordi Bernabeu
Format: Article
Language:Spanish
Published: Universidad Complutense de Madrid 2012-01-01
Series:Psicooncologia
Subjects:
Online Access:http://revistas.ucm.es/index.php/PSIC/article/view/37889
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author Águeda Sapiña
Adela Cañete
Tina Barahona
María Plasencia
María Moran
Olivia Prades
Davinia Fernandez
Laura Arjona
Paula Rubio
Jordi Bernabeu
author_facet Águeda Sapiña
Adela Cañete
Tina Barahona
María Plasencia
María Moran
Olivia Prades
Davinia Fernandez
Laura Arjona
Paula Rubio
Jordi Bernabeu
author_sort Águeda Sapiña
collection DOAJ
description Opsoclonus-ataxia, also called “dancing eye syndrome,” is a serious neurologic condition that is often a paraneoplastic manifestation of occult neuroblastoma in early childhood. Although survival is high with anti-tumoral treatment and immunosuppressive therapy, outcome generally includes significant developmental and behavioral sequelae. We report a case diagnosed at nine month of age, treated in our Unit and refered for a multidisciplinary neuropsychological rehabilitation when she was 4 year old.
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spelling doaj.art-f9c62c13bb9949b99f8dad8952dcaeef2022-12-21T22:41:37ZspaUniversidad Complutense de MadridPsicooncologia1696-72401988-82872012-01-0182-340542110.5209/rev_PSIC.2011.v8.n2-3.3788937733Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastomaÁgueda Sapiña0Adela Cañete1Tina Barahona2María Plasencia3María Moran4Olivia Prades5Davinia Fernandez6Laura Arjona7Paula Rubio8Jordi Bernabeu9Unidad de Daño Cerebral. Hermanas Hospitalarias, Valencia Oncología pediátrica. Hospital Universitario y Politécnico La Fe, ValenciaOncología pediátrica. Hospital Universitario y Politécnico La Fe, ValenciaOncología pediátrica. Hospital Universitario y Politécnico La Fe, Valencia Junta Asociada de Valencia de la Asociación Española Contra el Cancer.Unidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, ValenciaUnidad de Daño Cerebral. Hermanas Hospitalarias, Valencia Oncología pediátrica. Hospital Universitario y Politécnico La Fe, ValenciaOpsoclonus-ataxia, also called “dancing eye syndrome,” is a serious neurologic condition that is often a paraneoplastic manifestation of occult neuroblastoma in early childhood. Although survival is high with anti-tumoral treatment and immunosuppressive therapy, outcome generally includes significant developmental and behavioral sequelae. We report a case diagnosed at nine month of age, treated in our Unit and refered for a multidisciplinary neuropsychological rehabilitation when she was 4 year old.http://revistas.ucm.es/index.php/PSIC/article/view/37889Síndrome oposlonus-mioclonusataxianeuroblastomalate efectsneuropsicología pediátrica, síndrome paraneoplásico.
spellingShingle Águeda Sapiña
Adela Cañete
Tina Barahona
María Plasencia
María Moran
Olivia Prades
Davinia Fernandez
Laura Arjona
Paula Rubio
Jordi Bernabeu
Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma
Psicooncologia
Síndrome oposlonus-mioclonus
ataxia
neuroblastoma
late efects
neuropsicología pediátrica, síndrome paraneoplásico.
title Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma
title_full Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma
title_fullStr Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma
title_full_unstemmed Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma
title_short Case report: Opsoclonus-myoclonus syndrome associated with abdominal neuroblastoma
title_sort case report opsoclonus myoclonus syndrome associated with abdominal neuroblastoma
topic Síndrome oposlonus-mioclonus
ataxia
neuroblastoma
late efects
neuropsicología pediátrica, síndrome paraneoplásico.
url http://revistas.ucm.es/index.php/PSIC/article/view/37889
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