Atriofascicular Mahaim with Ebstein anomaly: A case report
We report a case of a 7-year-old girl with atriofascicular Mahaim (AFM) pathway concomitant with Ebstein's anomaly. The QRS wave showed left bundle branch block pattern on electrocardiogram. Holter electrocardiogram showed prolongation of the PR interval and QRS morphological change during sinu...
| Main Authors: | , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Wiley
2017-10-01
|
| Series: | Journal of Arrhythmia |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1880427617301266 |
| _version_ | 1819095828477771776 |
|---|---|
| author | Kazushi Ueshima, MD Yoshihide Nakamura, PhD Satoru Takeno, PhD Toshiharu Miyake, PhD Tsukasa Takemura, PhD |
| author_facet | Kazushi Ueshima, MD Yoshihide Nakamura, PhD Satoru Takeno, PhD Toshiharu Miyake, PhD Tsukasa Takemura, PhD |
| author_sort | Kazushi Ueshima, MD |
| collection | DOAJ |
| description | We report a case of a 7-year-old girl with atriofascicular Mahaim (AFM) pathway concomitant with Ebstein's anomaly. The QRS wave showed left bundle branch block pattern on electrocardiogram. Holter electrocardiogram showed prolongation of the PR interval and QRS morphological change during sinus tachycardia. An electrophysiological study demonstrated that the distal His potential appeared earlier than the proximal His potential, which suggested retrograde His conduction toward the atrioventricular node. Conduction from the Mahaim fiber to the His bundle was faster than that from the atrioventricular node towards the His bundle. The findings of this important case allowed a differential diagnosis between AFM and Wolff-Parkinson-White (WPW) syndrome. |
| first_indexed | 2024-12-21T23:49:30Z |
| format | Article |
| id | doaj.art-fa0030762bc54b26864e5894d8e33686 |
| institution | Directory Open Access Journal |
| issn | 1880-4276 |
| language | English |
| last_indexed | 2024-12-21T23:49:30Z |
| publishDate | 2017-10-01 |
| publisher | Wiley |
| record_format | Article |
| series | Journal of Arrhythmia |
| spelling | doaj.art-fa0030762bc54b26864e5894d8e336862022-12-21T18:45:58ZengWileyJournal of Arrhythmia1880-42762017-10-0133550851010.1016/j.joa.2017.06.007Atriofascicular Mahaim with Ebstein anomaly: A case reportKazushi Ueshima, MD0Yoshihide Nakamura, PhD1Satoru Takeno, PhD2Toshiharu Miyake, PhD3Tsukasa Takemura, PhD4Department of Pediatrics, Faculty of Medicine, Kindai University, JapanDepartment of Pediatrics, Faculty of Medicine, Kindai University, JapanDepartment of Pediatrics, Faculty of Medicine, Kindai University, JapanDepartment of Pediatrics, Faculty of Medicine, Nara Hospital, Kindai University, JapanDepartment of Pediatrics, Faculty of Medicine, Kindai University, JapanWe report a case of a 7-year-old girl with atriofascicular Mahaim (AFM) pathway concomitant with Ebstein's anomaly. The QRS wave showed left bundle branch block pattern on electrocardiogram. Holter electrocardiogram showed prolongation of the PR interval and QRS morphological change during sinus tachycardia. An electrophysiological study demonstrated that the distal His potential appeared earlier than the proximal His potential, which suggested retrograde His conduction toward the atrioventricular node. Conduction from the Mahaim fiber to the His bundle was faster than that from the atrioventricular node towards the His bundle. The findings of this important case allowed a differential diagnosis between AFM and Wolff-Parkinson-White (WPW) syndrome.http://www.sciencedirect.com/science/article/pii/S1880427617301266Atriofascicular MahaimEbstein anomalyElectrophysiology studyRadiofrequency catheter ablation |
| spellingShingle | Kazushi Ueshima, MD Yoshihide Nakamura, PhD Satoru Takeno, PhD Toshiharu Miyake, PhD Tsukasa Takemura, PhD Atriofascicular Mahaim with Ebstein anomaly: A case report Journal of Arrhythmia Atriofascicular Mahaim Ebstein anomaly Electrophysiology study Radiofrequency catheter ablation |
| title | Atriofascicular Mahaim with Ebstein anomaly: A case report |
| title_full | Atriofascicular Mahaim with Ebstein anomaly: A case report |
| title_fullStr | Atriofascicular Mahaim with Ebstein anomaly: A case report |
| title_full_unstemmed | Atriofascicular Mahaim with Ebstein anomaly: A case report |
| title_short | Atriofascicular Mahaim with Ebstein anomaly: A case report |
| title_sort | atriofascicular mahaim with ebstein anomaly a case report |
| topic | Atriofascicular Mahaim Ebstein anomaly Electrophysiology study Radiofrequency catheter ablation |
| url | http://www.sciencedirect.com/science/article/pii/S1880427617301266 |
| work_keys_str_mv | AT kazushiueshimamd atriofascicularmahaimwithebsteinanomalyacasereport AT yoshihidenakamuraphd atriofascicularmahaimwithebsteinanomalyacasereport AT satorutakenophd atriofascicularmahaimwithebsteinanomalyacasereport AT toshiharumiyakephd atriofascicularmahaimwithebsteinanomalyacasereport AT tsukasatakemuraphd atriofascicularmahaimwithebsteinanomalyacasereport |