Rhegmatogenous retinal detachment in Kniest Syndrome : Clinical model of abnormal vitreoretinal traction in children .
Introducing the management of non traumatic rhegmatogenous retinal detachment in pediatric patient in the context of a genetic syndrome associated with failure of type 2 collagen synthesis which manifests itself in ocular , hearing , facial , bone and joint abnormalities. We describe the clinical pr...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Pan-American Association of Ophthalmology
2012-03-01
|
| Series: | Vision Pan-America |
| Subjects: | |
| Online Access: | http://journals.sfu.ca/paao/index.php/journal/article/view/9 |
| Summary: | Introducing the management of non traumatic rhegmatogenous retinal detachment in pediatric patient in the context of a genetic syndrome associated with failure of type 2 collagen synthesis which manifests itself in ocular , hearing , facial , bone and joint abnormalities. We describe the clinical presentation of the picture and surgical repaire technique consisted of lensectomy , vitrectomy , peeling of vitreoretinal proliferation membranes , giant retinal tear management and prolonged tamponade by silicone oil. Long term clinical follow-up was carried out. We highlight this case report to be a therapeutic challenge in a deaf and high myopic child , with motor disabilities and atypical vitreoretinal disorders have generated difficulties in surgical resolution , there is also little scientific reference in world literature and represent a clinical model of abnormal vitreoretinal interaction |
|---|---|
| ISSN: | 2219-4665 2219-4673 |