Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in Indonesia
Lennox-Gastaut syndrome (LGS) is a form of severe epileptic encephalopathy in children. LGS with encephalomalacia cysts is rare in children. We report a six-year-old mentally retarded boy who was referred for an intractable seizure. Seizures were tonic, atonic, and dialeptic in frequency. EEG showed...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
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Rwanda Biomedical Centre (RBC)/Rwanda Health Communication Center
2022-09-01
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| Series: | Rwanda Medical Journal |
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| _version_ | 1818029401985515520 |
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| author | P. I. Gunawan W. Suryaningtyas |
| author_facet | P. I. Gunawan W. Suryaningtyas |
| author_sort | P. I. Gunawan |
| collection | DOAJ |
| description | Lennox-Gastaut syndrome (LGS) is a form of severe epileptic encephalopathy in children. LGS with encephalomalacia cysts is rare in children. We report a six-year-old mentally retarded boy who was referred for an intractable seizure. Seizures were tonic, atonic, and dialeptic in frequency. EEG showed generalized SSW discharges of 1.5-2 Hz, polyspikes, and burst suppression typical for LGS. Head MRI showed an encephalomalacia cyst in the right subcortical temporoparietal lobes with hemiatrophy in the right cerebral hemisphere. He was already treated with three antiepileptic drugs, but the seizures persisted. The patient was then performed right hemispherectomy and corpus callosotomy. It resulted in a good response. A combination of hemispherectomy and corpus callosotomy could be promising in this form of epilepsy disease. Seizure reduction was achieved and showed cognitive improvement and hemiparesis. |
| first_indexed | 2024-12-10T05:19:07Z |
| format | Article |
| id | doaj.art-facfa8d713514c2ca8d88f8dfab04573 |
| institution | Directory Open Access Journal |
| issn | 2410-8626 |
| language | English |
| last_indexed | 2024-12-10T05:19:07Z |
| publishDate | 2022-09-01 |
| publisher | Rwanda Biomedical Centre (RBC)/Rwanda Health Communication Center |
| record_format | Article |
| series | Rwanda Medical Journal |
| spelling | doaj.art-facfa8d713514c2ca8d88f8dfab045732022-12-22T02:00:53ZengRwanda Biomedical Centre (RBC)/Rwanda Health Communication CenterRwanda Medical Journal2410-86262022-09-0179358https://dx.doi.org/10.4314/rmj.v79i3.1Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in IndonesiaP. I. Gunawan0W. Suryaningtyas1Department of Child Health, Faculty of Medicine, Universitas Airlangga, Dr Soetomo General Academic Hospital, Surabaya, IndonesiaPediatric Neurosurgeon, Department of Neurosurgery, Faculty of Medicine, Universitas Airlangga, Dr Soetomo General Academic Hospital, Surabaya, IndonesiaLennox-Gastaut syndrome (LGS) is a form of severe epileptic encephalopathy in children. LGS with encephalomalacia cysts is rare in children. We report a six-year-old mentally retarded boy who was referred for an intractable seizure. Seizures were tonic, atonic, and dialeptic in frequency. EEG showed generalized SSW discharges of 1.5-2 Hz, polyspikes, and burst suppression typical for LGS. Head MRI showed an encephalomalacia cyst in the right subcortical temporoparietal lobes with hemiatrophy in the right cerebral hemisphere. He was already treated with three antiepileptic drugs, but the seizures persisted. The patient was then performed right hemispherectomy and corpus callosotomy. It resulted in a good response. A combination of hemispherectomy and corpus callosotomy could be promising in this form of epilepsy disease. Seizure reduction was achieved and showed cognitive improvement and hemiparesis.lennox-gastaut syndromediseaseencephalomalacia cysthemispherectomy |
| spellingShingle | P. I. Gunawan W. Suryaningtyas Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in Indonesia Rwanda Medical Journal lennox-gastaut syndrome disease encephalomalacia cyst hemispherectomy |
| title | Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in Indonesia |
| title_full | Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in Indonesia |
| title_fullStr | Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in Indonesia |
| title_full_unstemmed | Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in Indonesia |
| title_short | Hemispherectomy with corpus callosotomy in pediatric Lennox Gastaut Syndrome associated encephalomalacia cyst: The first case in Indonesia |
| title_sort | hemispherectomy with corpus callosotomy in pediatric lennox gastaut syndrome associated encephalomalacia cyst the first case in indonesia |
| topic | lennox-gastaut syndrome disease encephalomalacia cyst hemispherectomy |
| work_keys_str_mv | AT pigunawan hemispherectomywithcorpuscallosotomyinpediatriclennoxgastautsyndromeassociatedencephalomalaciacystthefirstcaseinindonesia AT wsuryaningtyas hemispherectomywithcorpuscallosotomyinpediatriclennoxgastautsyndromeassociatedencephalomalaciacystthefirstcaseinindonesia |