Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case report
Cardiac papillary fibroelastomas (CPFE) are exceptional primary benign cardiac tumours, affecting the heart valves. We report here the case of a 15-year-old boy in whom echocardiography performed for non-specific chest pain during follow-up for bicuspid aortic valve showed as accidental finding the...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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MDPI AG
2019-08-01
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| Series: | Clinics and Practice |
| Subjects: | |
| Online Access: | https://www.clinicsandpractice.org/index.php/cp/article/view/1135 |
| _version_ | 1811308231629209600 |
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| author | Sarah Dénes Benoît Daron Marie Behaeghe Marie-Christine Seghaye |
| author_facet | Sarah Dénes Benoît Daron Marie Behaeghe Marie-Christine Seghaye |
| author_sort | Sarah Dénes |
| collection | DOAJ |
| description | Cardiac papillary fibroelastomas (CPFE) are exceptional primary benign cardiac tumours, affecting the heart valves. We report here the case of a 15-year-old boy in whom echocardiography performed for non-specific chest pain during follow-up for bicuspid aortic valve showed as accidental finding the presence of a round mobile mass without stalk attached on the inferior side of the aortic valve. The mass did not cause any outflow tract obstruction or aortic insufficiency. ECG-gated cardiac computed tomography and magnetic resonance imaging allowed to suspect CPFE. Although the patient was asymptomatic, open cardiac surgery with elective surgical resection of the tumour were performed to avoid systematic emboli. Histology confirmed the diagnosis of CPFE. This is an exceptional case of acquired CPFE in a young patient with bicuspid aortic valve. Due the risk of systemic embolization, aortic- or coronary ostium obstruction, elective excision of such lesions is recommended. |
| first_indexed | 2024-04-13T09:19:29Z |
| format | Article |
| id | doaj.art-fbbab5c575dd4a97ba5cf613bc33804e |
| institution | Directory Open Access Journal |
| issn | 2039-7275 2039-7283 |
| language | English |
| last_indexed | 2024-04-13T09:19:29Z |
| publishDate | 2019-08-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Clinics and Practice |
| spelling | doaj.art-fbbab5c575dd4a97ba5cf613bc33804e2022-12-22T02:52:40ZengMDPI AGClinics and Practice2039-72752039-72832019-08-019310.4081/cp.2019.1135Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case reportSarah Dénes0Benoît Daron1Marie Behaeghe2Marie-Christine Seghaye3Pediatric Cardiology, Department of Pediatrics, University Hospital of LiègeDepartment of Pediatrics, Regional Hospital VerviersDepartment of Anatomo-Pathology, University Hospital of LeuvenPediatric Cardiology, Department of Pediatrics, University Hospital of LiègeCardiac papillary fibroelastomas (CPFE) are exceptional primary benign cardiac tumours, affecting the heart valves. We report here the case of a 15-year-old boy in whom echocardiography performed for non-specific chest pain during follow-up for bicuspid aortic valve showed as accidental finding the presence of a round mobile mass without stalk attached on the inferior side of the aortic valve. The mass did not cause any outflow tract obstruction or aortic insufficiency. ECG-gated cardiac computed tomography and magnetic resonance imaging allowed to suspect CPFE. Although the patient was asymptomatic, open cardiac surgery with elective surgical resection of the tumour were performed to avoid systematic emboli. Histology confirmed the diagnosis of CPFE. This is an exceptional case of acquired CPFE in a young patient with bicuspid aortic valve. Due the risk of systemic embolization, aortic- or coronary ostium obstruction, elective excision of such lesions is recommended.https://www.clinicsandpractice.org/index.php/cp/article/view/1135Cardiac papillary fibroelastomaBicuspid aortic valveChildren |
| spellingShingle | Sarah Dénes Benoît Daron Marie Behaeghe Marie-Christine Seghaye Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case report Clinics and Practice Cardiac papillary fibroelastoma Bicuspid aortic valve Children |
| title | Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case report |
| title_full | Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case report |
| title_fullStr | Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case report |
| title_full_unstemmed | Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case report |
| title_short | Cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent: A case report |
| title_sort | cardiac papillary fibroelastoma of a bicuspid aortic valve in an adolescent a case report |
| topic | Cardiac papillary fibroelastoma Bicuspid aortic valve Children |
| url | https://www.clinicsandpractice.org/index.php/cp/article/view/1135 |
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