Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic Management

Fourth ventricle outflow obstruction (FVOO) is a rare cause of obstructive hydrocephalus. In this study, we described a case of idiopathic FVOO with ileal atresia and laryngomalacia which was managed with endoscopic third ventriculostomy (ETV) and re-endoscopy. We also described the techniques of fe...

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Main Authors: Forhad H. Chowdhury, Mohammod Raziul Haque, Jalal Uddin Mohammod Rumi, Mohammod Samsul Arifin
Format: Article
Language:English
Published: Thieme Medical Publishers, Inc. 2020-06-01
Series:Indian Journal of Neurosurgery
Subjects:
Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0040-1710104
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author Forhad H. Chowdhury
Mohammod Raziul Haque
Jalal Uddin Mohammod Rumi
Mohammod Samsul Arifin
author_facet Forhad H. Chowdhury
Mohammod Raziul Haque
Jalal Uddin Mohammod Rumi
Mohammod Samsul Arifin
author_sort Forhad H. Chowdhury
collection DOAJ
description Fourth ventricle outflow obstruction (FVOO) is a rare cause of obstructive hydrocephalus. In this study, we described a case of idiopathic FVOO with ileal atresia and laryngomalacia which was managed with endoscopic third ventriculostomy (ETV) and re-endoscopy. We also described the techniques of fenestration of Liliequist membrane and partial removal of arachnoid membrane over dorsum sella (DS) to prevent closure of fenestration and recurrence of hydrocephalus. The patient was a 4-month-old infant presented with progressively increasing head size, feeding difficulty, respiratory distress, and tense fontanel. The infant had a history of laparotomy for ileal atresia. CT scan showed panventriculomegaly due to FVOO. ETV with fenestration of Liliequist membrane was done on emergency basis. After operation, the patient improved clinically and radiologically. Four weeks later, the patient returned with recurrent hydrocephalus. Endoscopic reoperation showed closure of fenestration in arachnoid membrane (Lilieqiest membrane). Endoscopic refenestration with partial excision of arachnoid on DS was done. The patient again recovered radiologically and clinically till last follow-up. In idiopathic FVOO, ETV with wide fenestration of Liliequist membrane, preferably with partial removal of arachnoid on DS, may be very useful in treating hydrocephalus (HCP) and preventing recurrent HCP even in infants.
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spelling doaj.art-fc97241a822d4cd9ae11d39d253aff8d2022-12-21T18:54:45ZengThieme Medical Publishers, Inc.Indian Journal of Neurosurgery2277-954X2277-91672020-06-0190321922410.1055/s-0040-1710104Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic ManagementForhad H. Chowdhury0Mohammod Raziul Haque1Jalal Uddin Mohammod Rumi2Mohammod Samsul Arifin3Department of Neurosurgery, National Institute of Neurosciences and Hospital, Dhaka, BangladeshDepartment of Neurosurgery, Dhaka Medical College Hospital, Dhaka, BangladeshDepartment of Neurosurgery, National Institute of Neurosciences and Hospital, Dhaka, BangladeshDepartment of Neurosurgery, Ibn Sina Specialized Hospital, Dhanmondi, Dhaka, BangladeshFourth ventricle outflow obstruction (FVOO) is a rare cause of obstructive hydrocephalus. In this study, we described a case of idiopathic FVOO with ileal atresia and laryngomalacia which was managed with endoscopic third ventriculostomy (ETV) and re-endoscopy. We also described the techniques of fenestration of Liliequist membrane and partial removal of arachnoid membrane over dorsum sella (DS) to prevent closure of fenestration and recurrence of hydrocephalus. The patient was a 4-month-old infant presented with progressively increasing head size, feeding difficulty, respiratory distress, and tense fontanel. The infant had a history of laparotomy for ileal atresia. CT scan showed panventriculomegaly due to FVOO. ETV with fenestration of Liliequist membrane was done on emergency basis. After operation, the patient improved clinically and radiologically. Four weeks later, the patient returned with recurrent hydrocephalus. Endoscopic reoperation showed closure of fenestration in arachnoid membrane (Lilieqiest membrane). Endoscopic refenestration with partial excision of arachnoid on DS was done. The patient again recovered radiologically and clinically till last follow-up. In idiopathic FVOO, ETV with wide fenestration of Liliequist membrane, preferably with partial removal of arachnoid on DS, may be very useful in treating hydrocephalus (HCP) and preventing recurrent HCP even in infants.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0040-1710104hydrocephalusfourth ventricle outflow obstructionendoscopic third ventriculostomyre-endoscopic procedure
spellingShingle Forhad H. Chowdhury
Mohammod Raziul Haque
Jalal Uddin Mohammod Rumi
Mohammod Samsul Arifin
Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic Management
Indian Journal of Neurosurgery
hydrocephalus
fourth ventricle outflow obstruction
endoscopic third ventriculostomy
re-endoscopic procedure
title Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic Management
title_full Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic Management
title_fullStr Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic Management
title_full_unstemmed Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic Management
title_short Fourth Ventricular Outflow Obstruction in an Infant with Ileal Atresia and Laryngomalacia: Endoscopic Management
title_sort fourth ventricular outflow obstruction in an infant with ileal atresia and laryngomalacia endoscopic management
topic hydrocephalus
fourth ventricle outflow obstruction
endoscopic third ventriculostomy
re-endoscopic procedure
url http://www.thieme-connect.de/DOI/DOI?10.1055/s-0040-1710104
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AT mohammodraziulhaque fourthventricularoutflowobstructioninaninfantwithilealatresiaandlaryngomalaciaendoscopicmanagement
AT jalaluddinmohammodrumi fourthventricularoutflowobstructioninaninfantwithilealatresiaandlaryngomalaciaendoscopicmanagement
AT mohammodsamsularifin fourthventricularoutflowobstructioninaninfantwithilealatresiaandlaryngomalaciaendoscopicmanagement