Restrictive cardiomyopathy and hypertrophic cardiomyopathy overlap: the importance of the phenotype

Restrictive cardiomyopathy (RCM) is defined on the basis of the haemodynamic finding of restrictive ventricular physiology. However, restrictive ventricular pathophysiology is also a feature of other subtypes of cardiomyopathy, including hypertrophic cardiomyopathy (HCM). Clinically and aetiological...

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Bibliographic Details
Main Authors: Juan Pablo Kaski, Elena Biagini, Massimo Lorenzini, Claudio Rapezzi, Perry Elliott
Format: Article
Language:English
Published: MDPI AG 2012-10-01
Series:Cardiogenetics
Subjects:
Online Access:http://www.pagepressjournals.org/index.php/cardiogen/article/view/594
Description
Summary:Restrictive cardiomyopathy (RCM) is defined on the basis of the haemodynamic finding of restrictive ventricular physiology. However, restrictive ventricular pathophysiology is also a feature of other subtypes of cardiomyopathy, including hypertrophic cardiomyopathy (HCM). Clinically and aetiologically, there is an overlap between RCM and HCM with restrictive physiology. However, the clinical distinction between these two entities can be an important pointer towards the underlying aetiology. This review highlights the importance of the recognition of the clinical phenotype as the first step in the classification of cardiomyopathies.
ISSN:2035-8253
2035-8148