Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram o...
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
| Published: |
Singapore Medical Association
2007
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| Subjects: | |
| Online Access: | http://irep.iium.edu.my/17108/1/Renal_cell_carcinoma_in_a_von_Hippel-.pdf |
| _version_ | 1825645692197011456 |
|---|---|
| author | Mohd Shah, Azarisman Shah K, Nor Azmi |
| author_facet | Mohd Shah, Azarisman Shah K, Nor Azmi |
| author_sort | Mohd Shah, Azarisman Shah |
| collection | IIUM |
| description | A 39-year-old man was diagnosed with
von Hippel-Lindau syndrome, which was
associated with retinal haemangioblastoma,
cervical cord haemangioblastoma and
bilateral renal cell carcinoma. He subsequently
underwent an arterial embolisation and
cervical laminectomy, following a spinal
angiogram of the cervical lesion. He also
had a right radical nephrectomy, with no
perioperative complications. However, on
admission for the left radical nephrectomy,
he was noted to have preoperative
hypertension. Further investigation
revealed an enlarged left adrenal gland
on abdominal computed tomography
scan and raised urinary catecholamines.
We discuss the risk of renal cell carcinoma
a nd ph a e oc h romoc y toma a r i s ing
concomitantly in von Hippel-Lindau
syndrome, and how best to investigate and
manage them. |
| first_indexed | 2024-03-05T22:51:31Z |
| format | Article |
| id | oai:generic.eprints.org:17108 |
| institution | International Islamic University Malaysia |
| language | English |
| last_indexed | 2024-03-05T22:51:31Z |
| publishDate | 2007 |
| publisher | Singapore Medical Association |
| record_format | dspace |
| spelling | oai:generic.eprints.org:171082012-01-26T09:31:10Z http://irep.iium.edu.my/17108/ Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? Mohd Shah, Azarisman Shah K, Nor Azmi RC254 Neoplasms. Tumors. Oncology (including Cancer) A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram of the cervical lesion. He also had a right radical nephrectomy, with no perioperative complications. However, on admission for the left radical nephrectomy, he was noted to have preoperative hypertension. Further investigation revealed an enlarged left adrenal gland on abdominal computed tomography scan and raised urinary catecholamines. We discuss the risk of renal cell carcinoma a nd ph a e oc h romoc y toma a r i s ing concomitantly in von Hippel-Lindau syndrome, and how best to investigate and manage them. Singapore Medical Association 2007 Article PeerReviewed application/pdf en http://irep.iium.edu.my/17108/1/Renal_cell_carcinoma_in_a_von_Hippel-.pdf Mohd Shah, Azarisman Shah and K, Nor Azmi (2007) Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? Singapore Medical Journal, 48(8) (779). ISSN 0037-5675 http://smj.sma.org.sg/smjcurrent.html |
| spellingShingle | RC254 Neoplasms. Tumors. Oncology (including Cancer) Mohd Shah, Azarisman Shah K, Nor Azmi Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? |
| title | Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? |
| title_full | Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? |
| title_fullStr | Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? |
| title_full_unstemmed | Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? |
| title_short | Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? |
| title_sort | renal cell carcinoma in a von hippel lindau syndrome when should pheochromocytoma be anticipated |
| topic | RC254 Neoplasms. Tumors. Oncology (including Cancer) |
| url | http://irep.iium.edu.my/17108/1/Renal_cell_carcinoma_in_a_von_Hippel-.pdf |
| work_keys_str_mv | AT mohdshahazarismanshah renalcellcarcinomainavonhippellindausyndromewhenshouldpheochromocytomabeanticipated AT knorazmi renalcellcarcinomainavonhippellindausyndromewhenshouldpheochromocytomabeanticipated |