Non-toxic ubiquitous over-expression of utrophin in the mdx mouse.
Duchenne muscular dystrophy (DMD) is an inherited, severe muscle wasting disease caused by the loss of the cytoskeletal protein, dystrophin. Patients usually die in their late teens or early twenties of cardiac or respiratory failure. We have previously demonstrated that the dystrophin related prote...
Autors principals: | Fisher, R, Tinsley, J, Phelps, SR, Squire, SE, Townsend, E, Martin, J, Davies, K |
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Format: | Journal article |
Idioma: | English |
Publicat: |
2001
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