Treatment-responsive pandysautonomia in an adolescent with ganglionic α3-AChR antibodies.

Autoimmune autonomic ganglionopathy (AAG) is a rare disorder that presents with pandysautonomia typically in middle age and elderly patients. AAG is typically associated with serum autoantibodies that bind to the alpha-3 subunit of the ganglionic acetylcholine receptor (α3-AChR Ab). We report a 13 y...

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Autori principali: Dale, R, Lang, B, Brilot, F, Polfrit, Y, Smith, G, Wong, M
Natura: Journal article
Lingua:English
Pubblicazione: 2012