Structural basis of fumarate hydratase deficiency.

Structural basis of fumarate hydratase deficiency.

Diğer sürümleri göster (2)

Fumarate hydratase catalyzes the stereospecific hydration across the olefinic double bond in fumarate leading to L-malate. The enzyme is expressed in mitochondrial and cytosolic compartments, and participates in the Krebs cycle in mitochondria, as well as in regulation of cytosolic fumarate levels....

Detaylı Bibliyografya
Asıl Yazarlar:	Picaud, S, Kavanagh, K, Yue, W, Lee, W, Muller-Knapp, S, Gileadi, O, Sacchettini, J, Oppermann, U
Materyal Türü:	Journal article
Dil:	English
Baskı/Yayın Bilgisi:	2011

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