Combined deficiencies of endosomal ganglioside neuraminidases 3 and 4 in mice cause lysosomal GM3 gangliosidosis

Eitemau Tebyg

• Combined deficiencies of endosomal ganglioside neuraminidases 3 and 4 in mice cause lysosomal GM3 gangliosidosis
  gan: Pshezhetsky, A, et al.
  Cyhoeddwyd: (2017)
• Neuraminidases 3 and 4 regulate neuronal function by catabolizing brain gangliosides
  gan: Pan, X, et al.
  Cyhoeddwyd: (2017)
• N-butyldeoxygalactonojirimycin reduces postnatal cerebellar ganglioside content in a mouse model of GM1 gangliosidosis
  gan: Kasperzyk, J, et al.
  Cyhoeddwyd: (2004)
• N-butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis.
  gan: Kasperzyk, J, et al.
  Cyhoeddwyd: (2004)
• "Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice" (vol 46, pg 744, 2004)
  gan: Kasperzyk, J, et al.
  Cyhoeddwyd: (2005)