Unnatural co-substrate-based rescue of enzyme activity in Refsum's disease resulting from mutations in R275 of phytanoyl-CoA hydroxylase.

Unnatural co-substrate-based rescue of enzyme activity in Refsum's disease resulting from mutations in R275 of phytanoyl-CoA hydroxylase.

Podrobná bibliografie
Hlavní autoři:	Lloyd, MD, Mukherji, M, Kershaw, N, MacKinnon, C, Schofield, C, Wierzbicki, A
Médium:	Journal article
Vydáno:	2000

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