Sleep phase delay in cystic fibrosis: a potential new manifestation of cystic fibrosis transmembrane regulator dysfunction

<strong>Background</strong> Cystic fibrosis (CF) transmembrane regulator (CFTR) protein dysfunction causes CF. Improving survival allows detection of increasingly subtle disease manifestations. CFTR dysfunction in the central nervous system (CNS) may disturb circadian rhythm and thus sl...

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Autors principals: Jensen, J, Jones, C, Kartsonaki, C, Packer, K, Adler, F, Liou, T
Format: Journal article
Idioma:English
Publicat: Elsevier 2017