N-butyldeoxygalactonojirimycin reduces postnatal cerebellar ganglioside content in a mouse model of GM1 gangliosidosis

N-butyldeoxygalactonojirimycin reduces postnatal cerebellar ganglioside content in a mouse model of GM1 gangliosidosis

ग्रंथसूची विवरण
मुख्य लेखकों:	Kasperzyk, J, d'Azzo, A, Platt, F, Seyfried, T
स्वरूप:	Conference item
प्रकाशित:	2004

समान संसाधन

N-butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis.
द्वारा: Kasperzyk, J, और अन्य
प्रकाशित: (2004)

"Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice" (vol 46, pg 744, 2004)
द्वारा: Kasperzyk, J, और अन्य
प्रकाशित: (2005)

N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal Sandhoff disease mice.
द्वारा: Baek, R, और अन्य
प्रकाशित: (2008)

N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal sandhoff diseased mice
द्वारा: Baek, R, और अन्य
प्रकाशित: (2004)

Erratum: Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice (Journal of Lipid Research (April 2004) 46 (744-751))
द्वारा: Kasperzyk, J, और अन्य
प्रकाशित: (2005)

Substrate deprivation therapy reduces brain ganglioside content and GM1 in neonatal storage disease mice
द्वारा: Kasperzyk, J, और अन्य
प्रकाशित: (2002)

Substrate reduction therapy reduces brain ganglioside GM2 in neonatal Sandhoff disease mice
द्वारा: Baek, R, और अन्य
प्रकाशित: (2005)

Central nervous system inflammation is a hallmark of pathogenesis in mouse models of GM1 and GM2 gangliosidosis.
द्वारा: Jeyakumar, M, और अन्य
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Beneficial effects of substrate reduction therapy in a mouse model of GM1 gangliosidosis.
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Therapeutic assessment of substrate deprivation using NB-DGJ in GM1 storage disease mice
द्वारा: Seyfried, T, और अन्य
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N -butyldeoxynojirimycin reduces growth and ganglioside content of experimental mouse brain tumours.
द्वारा: Ranes, M, और अन्य
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Combined deficiencies of endosomal ganglioside neuraminidases 3 and 4 in mice cause lysosomal GM3 gangliosidosis
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Combined deficiencies of endosomal ganglioside neuraminidases 3 and 4 in mice cause lysosomal GM3 gangliosidosis
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Altered expression of ganglioside metabolizing enzymes results in GM3 ganglioside accumulation in cerebellar cells of a mouse model of juvenile neuronal ceroid lipofuscinosis
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Effects of substrate deprivation therapy on brain lipids in neonatal GML storage disease mice
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Therapeutic developments for neurodegenerative GM1 gangliosidosis
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Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease.
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GM1 ganglioside-independent intoxication by Cholera toxin
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N-butyldeoxygalactonojirimycin: a more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo.
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Persistent elevations of alkaline phosphatase as an early indicator of GM1 gangliosidosis
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GM1 - gangliosidosis in a Nigerian infant: A case report
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Pathological findings of central nervous system, two GM1 gangliosidosis autopsy cases
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