N-butyldeoxygalactonojirimycin reduces postnatal cerebellar ganglioside content in a mouse model of GM1 gangliosidosis

N-butyldeoxygalactonojirimycin reduces postnatal cerebellar ganglioside content in a mouse model of GM1 gangliosidosis

Bibliografiska uppgifter
Huvudupphovsmän:	Kasperzyk, J, d'Azzo, A, Platt, F, Seyfried, T
Materialtyp:	Conference item
Publicerad:	2004

Liknande verk

N-butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis.
av: Kasperzyk, J, et al.
Publicerad: (2004)

"Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice" (vol 46, pg 744, 2004)
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N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal Sandhoff disease mice.
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N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal sandhoff diseased mice
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Erratum: Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice (Journal of Lipid Research (April 2004) 46 (744-751))
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Substrate deprivation therapy reduces brain ganglioside content and GM1 in neonatal storage disease mice
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Substrate reduction therapy reduces brain ganglioside GM2 in neonatal Sandhoff disease mice
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Therapeutic assessment of substrate deprivation using NB-DGJ in GM1 storage disease mice
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Effects of substrate deprivation therapy on brain lipids in neonatal GML storage disease mice
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Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease.
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Elevation of ganglioside degradation pathway drives GM2 and GM3 within amyloid plaques in a transgenic mouse model of Alzheimer's disease
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Pathological findings of central nervous system, two GM1 gangliosidosis autopsy cases
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Mutations in B4GALNT1 (GM2 synthase) underlie a new disorder of ganglioside biosynthesis
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