Role of phytanoyl-CoA 2-hydroxylase in phytanic acid metabolism.

Role of phytanoyl-CoA 2-hydroxylase in phytanic acid metabolism.

Bibliographic Details
Main Authors:	Lloyd, MD, Mukherji, M, Kershaw, N, Chien, W, Wierzbicki, A, Schofield, C
Format:	Conference item
Published:	2003

Similar Items

Utilization of sterol carrier protein-2 by phytanoyl-CoA 2-hydroxylase in the peroxisomal alpha oxidation of phytanic acid.
by: Mukherji, M, et al.
Published: (2002)

Studies on phytanoyl-CoA 2-hydroxylase and synthesis of phytanoyl-coenzyme A.
by: Kershaw, N, et al.
Published: (2001)

Structure-function analysis of phytanoyl-CoA 2-hydroxylase mutations causing Refsum's disease.
by: Mukherji, M, et al.
Published: (2001)

'Chemical co-substrate rescue' of phytanoyl-CoA 2-hydroxylase mutants causing Refsum's Disease
by: Mukherji, M, et al.
Published: (2001)

Unnatural co-substrate-based rescue of enzyme activity in Refsum's disease resulting from mutations in R275 of phytanoyl-CoA hydroxylase.
by: Lloyd, MD, et al.
Published: (2000)

Studies on the specificity of unprocessed and mature forms of phytanoyl-CoA 2-hydroxylase and mutation of the iron binding ligands.
by: Searls, T, et al.
Published: (2005)

Structural and mechanistic studies on the peroxisomal oxygenase phytanoyl-CoA 2-hydroxylase (PhyH).
by: Schofield, C, et al.
Published: (2007)

Structure of human phytanoyl-CoA 2-hydroxylase identifies molecular mechanisms of Refsum disease.
by: McDonough, M, et al.
Published: (2005)

Crystal structure of PHYHD1A, a 2OG oxygenase related to phytanoyl-CoA hydroxylase.
by: Zhang, Z, et al.
Published: (2011)

Refsum's disease: a peroxisomal disorder affecting phytanic acid alpha-oxidation.
by: Wierzbicki, A, et al.
Published: (2002)

Phytanic acid, an inconclusive phytol metabolite: A review
by: Muhammad Torequl Islam, et al.
Published: (2023-01-01)

The chemical biology of branched-chain lipid metabolism.
by: Mukherji, M, et al.
Published: (2003)

Plasma phytanic acid concentration and risk of prostate cancer: results from the European Prospective Investigation into Cancer and Nutrition.
by: Price, A, et al.
Published: (2010)

Plasma phytanic acid concentration and risk of prostate cancer: Results from the European prospective investigation into cancer and nutrition
by: Price, A, et al.
Published: (2010)

The Pathophysiological Role of CoA
by: Aleksandra Czumaj, et al.
Published: (2020-11-01)

Phytanic Acid Intake and Lifestyle Modifications on Quality of Life in Individuals with Adult Refsum Disease: A Retrospective Survey Analysis
by: Jeffrey J. Li, et al.
Published: (2023-05-01)

Phytanic acid: measurement of plasma concentrations by gas-liquid chromatography-mass spectrometry analysis and associations with diet and other plasma fatty acids.
by: Allen, N, et al.
Published: (2008)

The Role of Acyl-CoA β-Oxidation in Brain Metabolism and Neurodegenerative Diseases
by: Sylwia Szrok-Jurga, et al.
Published: (2023-09-01)

Acyl-CoA-dependent and acyl-CoA-independent avocado acyltransferases positively influence oleic acid content in nonseed triacylglycerols
by: Jyoti Behera, et al.
Published: (2023-01-01)

Diversion of Acetyl CoA to 3-Methylglutaconic Acid Caused by Discrete Inborn Errors of Metabolism
by: Dylan E. Jones, et al.
Published: (2022-04-01)

Acyl-CoA synthase ACSL4: an essential target in ferroptosis and fatty acid metabolism
by: Kaiyue Ding, et al.
Published: (2023-11-01)

Stearoyl-CoA Desaturase-1: Is It the Link between Sulfur Amino Acids and Lipid Metabolism?
by: Soraia Poloni, et al.
Published: (2015-06-01)

Use of methylmalonyl‐CoA epimerase in enhancing crotonase stereoselectivity
by: Hamed, R, et al.
Published: (2015)

Acetyl-CoA metabolism as a therapeutic target for cancer
by: Guo Chen, et al.
Published: (2023-12-01)

Signalling hypoxia by HIF hydroxylases.
by: Schofield, C, et al.
Published: (2005)

Oxygen sensing by HIF hydroxylases.
by: Schofield, C, et al.
Published: (2004)

Outlook: Membrane junctions enable the metabolic trapping of fatty acids by intracellular acyl-CoA synthetases
by: Joachim eFuellekrug, et al.
Published: (2012-10-01)

The Physiological and Pathological Role of Acyl-CoA Oxidation
by: Sylwia Szrok-Jurga, et al.
Published: (2023-10-01)

Characteristics of long‐chain acyl‐CoA synthetases in metabolism and cancer
by: Linlin Zhang, et al.
Published: (2023-06-01)

Acetyl-CoA Metabolism and Histone Acetylation in the Regulation of Aging and Lifespan
by: Patrick C. Bradshaw
Published: (2021-04-01)

Metabolic Engineering Design Strategies for Increasing Acetyl-CoA Flux
by: Jason T. Ku, et al.
Published: (2020-04-01)

Metabolic and Cellular Compartments of Acetyl-CoA in the Healthy and Diseased Brain
by: Agnieszka Jankowska-Kulawy, et al.
Published: (2022-09-01)

Pathway engineering and metabolic flux analysis of acetyl-coA biosynthesis.
by: Hee, Kai Sheng.
Published: (2011)

Biochemistry of the hypoxia-inducible factor hydroxylases
by: Fiorini, G, et al.
Published: (2024)

CoA in Health and Disease
by: Pawel Dobrzyn
Published: (2022-04-01)

Erratum: Acyl-CoA-dependent and acyl-CoA-independent avocado acyltransferases positively influence oleic acid content in nonseed triacylglycerols
by: Frontiers Production Office
Published: (2023-02-01)

Acetyl-CoA synthetase (ACSS2) does not generate butyryl- and crotonyl-CoA
by: Nour Zeaiter, et al.
Published: (2024-03-01)

A structural mapping of mutations causing succinyl-CoA:3-ketoacid CoA transferase (SCOT) deficiency
by: Shafqat, N, et al.
Published: (2013)

A structural mapping of mutations causing succinyl-CoA:3-ketoacid CoA transferase (SCOT) deficiency.
by: Shafqat, N, et al.
Published: (2013)

Therapeutic manipulation of the HIF hydroxylases.
by: Nagel, S, et al.
Published: (2010)