Analysis of giant cell tumour of bone cells for Noonan syndrome/cherubism-related mutations.

BACKGROUND: Giant cell tumour of bone (GCTB) is an osteolytic tumour which contains numerous osteoclast-like giant cells and a proliferation of mononuclear stromal cells (MSC). Giant cell-rich osteolytic lesions can also develop in the jaw bones in Noonan syndrome, a cherubism-like developmental abn...

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Autori principali: Moskovszky, L, Idowu, B, Taylor, R, Mertens, F, Athanasou, N, Flanagan, A
Natura: Journal article
Lingua:English
Pubblicazione: 2013