Genetic, structural, and functional analysis of pathogenic variations causing methylmalonyl-CoA epimerase deficiency

Human methylmalonyl-CoA epimerase (MCEE) catalyzes the interconversion of d-methylmalonyl-CoA and l-methylmalonyl-CoA in propionate catabolism. Autosomal recessive pathogenic variations in MCEE reportedly cause methylmalonic aciduria (MMAuria) in eleven patients. We investigated a cohort of 150 indi...

詳細記述

書誌詳細
主要な著者: Heuberger, K, Bailey, HJ, Burda, P, Chaikuad, A, Krysztofinska, E, Suormala, T, Bürer, C, Lutz, S, Fowler, B, Froese, DS, Yue, WW, Baumgartner, MR
フォーマット: Journal article
言語:English
出版事項: Elsevier 2019