Update in understanding common variable immunodeficiency disorders (CVIDs) and the management of patients with these conditions.

Update in understanding common variable immunodeficiency disorders (CVIDs) and the management of patients with these conditions.

The common variable immunodeficiency disorders are a mixed group of heterogeneous conditions linked by lack of immunoglobulin production and primary antibody failure. This variability results in difficulty in making coherent sense of either immunopathogenesis or the role of various genetic abnormali...

Disgrifiad llawn

Manylion Llyfryddiaeth
Prif Awduron:	Chapel, H, Cunningham-Rundles, C
Fformat:	Journal article
Iaith:	English
Cyhoeddwyd:	2009

Eitemau Tebyg

Common Variable Immunodeficiency Disorders (CVID) – diagnoses of exclusion, especially combined immune defects
gan: Chapel, H
Cyhoeddwyd: (2016)

Editorial: Updates on the pathogenesis of common variable immunodeficiency (CVID)
gan: Timi Martelius, et al.
Cyhoeddwyd: (2023-01-01)

2153 The plasma contact system and its role in common variable immunodeficiency (CVID): An explorative study
gan: Tukisa Smith, et al.
Cyhoeddwyd: (2018-06-01)

Assessing Disease Severity in Common Variable Immunodeficiency Disorders (CVID) and CVID-Like Disorders
gan: Rohan Ameratunga, et al.
Cyhoeddwyd: (2018-09-01)

Autoimmune Cytopenias In Common Variable Immunodeficiency (CVID)
gan: Roshini Sarah Abraham, et al.
Cyhoeddwyd: (2012-07-01)

Pathogenesis of autoimmunity in common variable immunodeficiency (CVID)
gan: Klaus eWarnatz, et al.
Cyhoeddwyd: (2012-07-01)

Investigation of NOD2 polymorphisms in Common Variable Immunodeficiency (CVID) and its granulomatous and enteropathic manifestations
gan: Staples, E, et al.
Cyhoeddwyd: (2008)

Outcomes of splenectomy in patients with common variable immunodeficiency (CVID): a survey of 45 patients.
gan: Wong, G, et al.
Cyhoeddwyd: (2013)

Non-infectious Complications of Common Variable Immunodeficiency: Updated Clinical Spectrum, Sequelae, and Insights to Pathogenesis
gan: Hsi-en Ho, et al.
Cyhoeddwyd: (2020-02-01)

Fatal Puumala Hantavirus Infection in a Patient with Common Variable Immunodeficiency (CVID)
gan: Philipp Steininger, et al.
Cyhoeddwyd: (2023-01-01)

All Patients With Common Variable Immunodeficiency Disorders (CVID) Should Be Routinely Offered Diagnostic Genetic Testing
gan: Rohan Ameratunga, et al.
Cyhoeddwyd: (2019-11-01)

Management of liver disease and portal hypertension in common variable immunodeficiency (CVID)Key points
gan: Lukas S. Baumert, et al.
Cyhoeddwyd: (2023-11-01)

Measurement of peripheral B cell subpopulations in common variable immunodeficiency (CVID) using a whole blood method.
gan: Ferry, B, et al.
Cyhoeddwyd: (2005)

Confirmation and improvement of criteria for clinical phenotyping in common variable immunodeficiency disorders in replicate cohorts.
gan: Chapel, H, et al.
Cyhoeddwyd: (2012)

Confirmation and improvement of criteria for clinical phenotyping in common variable immunodeficiency disorders in replicate cohorts
gan: Chapel, H, et al.
Cyhoeddwyd: (2012)

Cytokine dysregulation despite immunoglobulin replacement therapy in common variable immunodeficiency (CVID)
gan: Remo Poto, et al.
Cyhoeddwyd: (2023-09-01)

Granulomatous Lymphocytic Interstitial Lung Disease (GLILD) in Common Variable Immunodeficiency (CVID)
gan: Nico Hustings, et al.
Cyhoeddwyd: (2022-12-01)

The impact of rare and low-frequency genetic variants in common variable immunodeficiency (CVID)
gan: Atil Bisgin, et al.
Cyhoeddwyd: (2021-04-01)

The critical role of histology in distinguishing sarcoidosis from common variable immunodeficiency disorder (CVID) in a patient with hypogammaglobulinemia
gan: Rohan Ameratunga, et al.
Cyhoeddwyd: (2019-12-01)

Skewed distribution of circulating activated natural killer T (NKT) cells in patients with common variable immunodeficiency disorders (CVID).
gan: Karina I Carvalho, et al.
Cyhoeddwyd: (2010-09-01)

Impaired Memory B-Cell Response to Influenza Immunization in Patients With Common Variable Immunodeficiency (CVID)
gan: Wei Zhan, et al.
Cyhoeddwyd: (2021-10-01)

The Natural History of Untreated Primary Hypogammaglobulinemia in Adults: Implications for the Diagnosis and Treatment of Common Variable Immunodeficiency Disorders (CVID)
gan: Rohan Ameratunga, et al.
Cyhoeddwyd: (2019-07-01)

Outcomes of splenectomy in patients with common variable immunodeficiency (CVID): a survey of 45 patients (vol 172, pg 63, 2013)
gan: Wong, G, et al.
Cyhoeddwyd: (2013)

Dissecting the group of common variable immunodeficiency disorders.
gan: Aslam, A, et al.
Cyhoeddwyd: (2009)

Genetics and clinical phenotypes in common variable immunodeficiency
gan: Charlotte Cunningham-Rundles, et al.
Cyhoeddwyd: (2024-01-01)

Interstitial lung diseases (ILD) in common variable immunodeficiency (CVID) patients: a study from Iran
gan: Ghamartaj Khanbabaee, et al.
Cyhoeddwyd: (2024-07-01)

Evaluation of Mutation in B cell Maturation Antigen (BCMA) Gene in Patients with Common Variable Immunodeficiency (CVID)
gan: Mahboobeh Ansari, et al.
Cyhoeddwyd: (2016-07-01)

Burden of copy number variation in common variable immunodeficiency
gan: Keller, M, et al.
Cyhoeddwyd: (2014)

Burden of copy number variation in common variable immunodeficiency.
gan: Keller, M, et al.
Cyhoeddwyd: (2014)

Levofloxacin and moxifloxacin resistant Haemophilus influenzae in a patient with common variable immunodeficiency (CVID): a case report
gan: CT Hapuarachchi, et al.
Cyhoeddwyd: (2018-05-01)

Current clinical spectrum of common variable immunodeficiency in Spain: The multicentric nationwide GTEM-SEMI-CVID registry
gan: Marta Dafne Cabañero-Navalon, et al.
Cyhoeddwyd: (2022-10-01)

Interstitial Lung Disease in Common Variable Immunodeficiency
gan: Joao Pedro Lopes, et al.
Cyhoeddwyd: (2021-03-01)

Increased Expression of B Lymphocyte Induced Maturation Protein 1 (BLIMP1) in Patients with Common Variable Immunodeficiency (CVID)
gan: Shockrollah Farrokhi, et al.
Cyhoeddwyd: (2020-08-01)

Spectrum of lymphoproliferation in common variable immunodeficiency disorders - review of the literature
gan: da Silva, S, et al.
Cyhoeddwyd: (2009)

The Central Nervous System Effects and Mimicry of Common Variable Immunodeficiency (CVID): A Case Report with Literature Review
gan: Sohail Farshad, et al.
Cyhoeddwyd: (2019-01-01)

Patients With Common Variable Immunodeficiency (CVID) Show Higher Gut Bacterial Diversity and Levels of Low-Abundance Genes Than the Healthy Housemates
gan: Juraj Bosák, et al.
Cyhoeddwyd: (2021-05-01)

Primary immunodeficiencies: 2009 update.
gan: Notarangelo, L, et al.
Cyhoeddwyd: (2009)

Lymphoid Proliferations of Indeterminate Malignant Potential arising in Adults with Common Variable Immunodeficiency Disorders: Unusual Case Studies and Immunohistological Review in the Light of Possible Causative Events
gan: da Silva, S, et al.
Cyhoeddwyd: (2011)

Lymphoid proliferations of indeterminate malignant potential arising in adults with common variable immunodeficiency disorders: unusual case studies and immunohistological review in the light of possible causative events.
gan: da Silva, S, et al.
Cyhoeddwyd: (2011)

Lymphocytic interstitial prieumonitis in common variable immunodeficiency disorders: A comparison with HIV
gan: Arnold, D, et al.
Cyhoeddwyd: (2007)