Hepcidin is suppressed by erythropoiesis in hemoglobin E β-thalassemia and β-thalassemia trait.

Hepcidin is suppressed by erythropoiesis in hemoglobin E β-thalassemia and β-thalassemia trait.

HbE β-thalassemia is the most common severe thalassemia syndrome across Asia, and millions are carriers. Clinical heterogeneity in HbE β-thalassemia is incompletely explained by genotype, and the interaction of phenotypic variation with hepcidin is unknown. The effect of thalassemia carriage on hepc...

Cur síos iomlán

Sonraí bibleagrafaíochta
Príomhchruthaitheoirí:	Jones, E, Pasricha, SR, Allen, A, Evans, P, Fisher, C, Wray, K, Premawardhena, A, Bandara, D, Perera, A, Webster, C, Sturges, P, Olivieri, N, St Pierre, T, Armitage, A, Porter, J, Weatherall, D, Drakesmith, H
Formáid:	Journal article
Teanga:	English
Foilsithe / Cruthaithe:	2014

Míreanna comhchosúla

Differences in the erythropoiesis-hepcidin-iron store axis between hemoglobin H disease and β-thalassemia intermedia
de réir: Raffaella Origa, et al.
Foilsithe / Cruthaithe: (2015-05-01)

Ineffective Erythropoiesis in β-Thalassemia
de réir: Jean-Antoine Ribeil, et al.
Foilsithe / Cruthaithe: (2013-01-01)

Adaptation to anemia in hemoglobin E-β thalassemia (Blood (2010) 116, 24 (5368-5370))
de réir: Allen, A, et al.
Foilsithe / Cruthaithe: (2011)

Challenging the Erythropoiesis Paradigm in β-Thalassemia
de réir: Francesca Vinchi, et al.
Foilsithe / Cruthaithe: (2020-10-01)

Adaptation to anemia in hemoglobin E-ß thalassemia.
de réir: Allen, A, et al.
Foilsithe / Cruthaithe: (2010)

Regulation of hepcidin by erythropoiesis: The story so far.
de réir: Pasricha, S, et al.
Foilsithe / Cruthaithe: (2016)

The interactions between ineffective erythropoiesis and ferroptosis in β-thalassemia
de réir: Siyang Lin, et al.
Foilsithe / Cruthaithe: (2024-02-01)

Liver iron concentrations and urinary hepcidin in β-thalassemia
de réir: Raffaella Origa, et al.
Foilsithe / Cruthaithe: (2007-05-01)

𝛽-Thalassemia: HiJAKing Ineffective Erythropoiesis and Iron Overload
de réir: Luca Melchiori, et al.
Foilsithe / Cruthaithe: (2010-01-01)

Adaptation to anemia in hemoglobin E-beta thalassemia (vol 116, pg 5368, 2011)
de réir: Allen, A, et al.
Foilsithe / Cruthaithe: (2011)

Hepcidin and HFE Polymorphisms and Ferritin Level in β-Thalassemia Major
de réir: Kiavash Fekri, et al.
Foilsithe / Cruthaithe: (2019-01-01)

Hepcidin Levels in Multi Transfused β Thalassemia Major Patients
de réir: Muhammad Jawad
Foilsithe / Cruthaithe: (2016-09-01)

Hemoglobin E-beta-thalassemia: Progress report from the International Study Group.
de réir: Premawardhena, A, et al.
Foilsithe / Cruthaithe: (2005)

THALIDOMIDE AMELIORATES ERYTHROPOIESIS AND IRON HOMEOSTASIS IN TRANSFUSION-DEPENDENT β-THALASSEMIA
de réir: Kun Yang, et al.
Foilsithe / Cruthaithe: (2024-01-01)

A mechanism of ineffective erythropoiesis in β-thalassemia/Hb E disease
de réir: Pathrapol Lithanatudom, et al.
Foilsithe / Cruthaithe: (2010-05-01)

Minihepcidins improve ineffective erythropoiesis and splenomegaly in a new mouse model of adult β-thalassemia major
de réir: Carla Casu, et al.
Foilsithe / Cruthaithe: (2020-07-01)

DIFFERENCES IN HEPCIDIN REGULATION DISTINGUISH MILD AND SEVERE PHENOTYPES OF E-BETA THALASSAEMIA
de réir: Jones, E, et al.
Foilsithe / Cruthaithe: (2013)

MOLECULAR ANALYSIS OF NON-TRANSFUSION DEPENDENT THALASSEMIA ASSOCIATED WITH HEMOGLOBIN E-β-THALASSEMIA DISEASE WITHOUT α--THALASSEMIA
de réir: Paramee Phanrahan, et al.
Foilsithe / Cruthaithe: (2019-06-01)

Antibodies against the erythroferrone N-terminal domain prevent hepcidin suppression and ameliorate murine thalassemia
de réir: Arezes, J, et al.
Foilsithe / Cruthaithe: (2020)

Erythropoiesis is not equally suppressed in transfused males and females with β-thalassemia major: are there clinical implications?
de réir: Greg Hapgood, et al.
Foilsithe / Cruthaithe: (2015-08-01)

Β-Thalassemia in Iran
de réir: M Haghi, et al.
Foilsithe / Cruthaithe: (2010-07-01)

Hepcidin detects iron deficiency in Sri Lankan adolescents with a high burden of hemoglobinopathy: A diagnostic test accuracy study
de réir: Wray, K, et al.
Foilsithe / Cruthaithe: (2017)

Multiplex Mutagenically Separated PCR: Diagnosis of β-Thalassemia and Hemoglobin Variants
de réir: J.-G. Chang, et al.
Foilsithe / Cruthaithe: (1997-03-01)

Unresolved laboratory issues of the heterozygous state of β-thalassemia: a literature review
de réir: Shyamali Thilakarathne, et al.
Foilsithe / Cruthaithe: (2023-06-01)

Abnormal hemoglobin anti-Lepore Hong Kong compound with β0-thalassemia ameliorate thalassemia severity when co-inherited with α-thalassemia
de réir: Xiuqin Bao, et al.
Foilsithe / Cruthaithe: (2024-03-01)

What regulates hepcidin in poly-transfused β-Thalassemia Major: Erythroid drive or store drive?
de réir: Richa Chauhan, et al.
Foilsithe / Cruthaithe: (2014-01-01)

Anemia in β-thalassemia patients targets hepatic hepcidin transcript levels independently of iron metabolism genes controlling hepcidin expression
de réir: Emilie Camberlein, et al.
Foilsithe / Cruthaithe: (2008-01-01)

Thalassemia in Sri Lanka: a progress report.
de réir: Premawardhena, A, et al.
Foilsithe / Cruthaithe: (2004)

Thalassemia intermedia in HbH-CS disease with compound heterozygosity for β-thalassemia: challenges in hemoglobin analysis and clinical diagnosis
de réir: Tan, Mary Anne Jin Ai, et al.
Foilsithe / Cruthaithe: (2009)

Ferroportin inhibitor vamifeport ameliorates ineffective erythropoiesis in a mouse model of β-thalassemia with blood transfusions
de réir: Natarajaswamy Kalleda, et al.
Foilsithe / Cruthaithe: (2023-05-01)

Hepcidin gene polymorphisms and iron overload in β-thalassemia major patients refractory to iron chelating therapy
de réir: Parinaz Zarghamian, et al.
Foilsithe / Cruthaithe: (2020-04-01)

Prevalence and mutations of β-thalassemia trait and abnormal hemoglobins in premarital screening in Çanakkale province, Turkey
de réir: Uludağ A, et al.
Foilsithe / Cruthaithe: (2016-06-01)

Polycythemia vera in patients of beta-thalassemia trait and stress erythropoiesis
de réir: Afaq A. Khan, et al.
Foilsithe / Cruthaithe: (2023-02-01)

Recent advances in β-thalassemias
de réir: Antonio Cao, et al.
Foilsithe / Cruthaithe: (2011-05-01)

β-Thalassemia Intermedia: Interaction of α-Globin Gene Triplication With β-thalassemia Heterozygous in Spain
de réir: Paloma Ropero, et al.
Foilsithe / Cruthaithe: (2022-03-01)

Echocardiografic abnormalities in patients with sickle cell/β-thalassemia do not depend on the β-thalassemia phenotype
de réir: Bruno Deltreggia Benites, et al.
Foilsithe / Cruthaithe: (2019-04-01)

Association of NRAMP1 Gene Polymorphism with Hemoglobin and Iron Parameters in Patients with β-Thalassemia Major
de réir: Sameh M. Nahi, et al.
Foilsithe / Cruthaithe: (2024-09-01)

Interaction of malaria with a common form of severe thalassemia in an Asian population.
de réir: O'Donnell, A, et al.
Foilsithe / Cruthaithe: (2009)

Activation of STAT and SMAD Signaling Induces Hepcidin Re-Expression as a Therapeutic Target for β-Thalassemia Patients
de réir: Hanan Kamel M. Saad, et al.
Foilsithe / Cruthaithe: (2022-01-01)

Effective screening of hemoglobin Constant Spring and hemoglobin Paksé with several forms of α- and β-thalassemia in an area with a high prevalence and heterogeneity of thalassemia using capillary electrophoresis
de réir: Sitthichai Panyasai, et al.
Foilsithe / Cruthaithe: (2023-08-01)