Substrate reduction therapy reduces brain ganglioside GM2 in neonatal Sandhoff disease mice

Substrate reduction therapy reduces brain ganglioside GM2 in neonatal Sandhoff disease mice

التفاصيل البيبلوغرافية
المؤلفون الرئيسيون:	Baek, R, Kasperzyk, J, Platt, F, Seyfried, T
التنسيق:	Conference item
منشور في:	2005

مواد مشابهة

N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal Sandhoff disease mice.
حسب: Baek, R, وآخرون
منشور في: (2008)

N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal sandhoff diseased mice
حسب: Baek, R, وآخرون
منشور في: (2004)

Substrate deprivation therapy reduces brain ganglioside content and GM1 in neonatal storage disease mice
حسب: Kasperzyk, J, وآخرون
منشور في: (2002)

Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice
حسب: J.L. Kasperzyk, وآخرون
منشور في: (2005-04-01)

"Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice" (vol 46, pg 744, 2004)
حسب: Kasperzyk, J, وآخرون
منشور في: (2005)

N-butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis.
حسب: Kasperzyk, J, وآخرون
منشور في: (2004)

Erratum: Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice (Journal of Lipid Research (April 2004) 46 (744-751))
حسب: Kasperzyk, J, وآخرون
منشور في: (2005)

N-butyldeoxygalactonojirimycin reduces postnatal cerebellar ganglioside content in a mouse model of GM1 gangliosidosis
حسب: Kasperzyk, J, وآخرون
منشور في: (2004)

Effects of substrate deprivation therapy on brain lipids in neonatal GML storage disease mice
حسب: Kasperzyk, J, وآخرون
منشور في: (2003)

Restricted ketogenic diet enhances the therapeutic action of N-butyldeoxynojirimycin towards brain GM2 accumulation in adult Sandhoff disease mice.
حسب: Denny, C, وآخرون
منشور في: (2010)

Therapeutic assessment of substrate deprivation using NB-DGJ in GM1 storage disease mice
حسب: Seyfried, T, وآخرون
منشور في: (2003)

Substrate reduction therapy in Sandhoff disease: Evidence for improvement in nervous function in patients treated with miglustat
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Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease.
حسب: Andersson, U, وآخرون
منشور في: (2004)

Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease
حسب: Ulrika Andersson, وآخرون
منشور في: (2004-08-01)

Elevated ganglioside GM2 activator (GM2A) in human brain tissue reduces neurite integrity and spontaneous neuronal activity
حسب: Yi-Chen Hsieh, وآخرون
منشور في: (2022-09-01)

Enhanced survival in Sandhoff disease mice receiving a combination of substrate deprivation therapy and bone marrow transplantation.
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Pathophysiology of Ganglioside GM1 in Ischemic Stroke: Ganglioside GM1: A Critical Review
حسب: Wenchao Zhang, وآخرون
منشور في: (2019-06-01)

Thematic Review Series: Sphingolipids. Ganglioside GM3 suppresses the proangiogenic effects of vascular endothelial growth factor and ganglioside GD1a*
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منشور في: (2014-03-01)

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The relationship between depletion of brain GM1 ganglioside and Parkinson's disease
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منشور في: (2023-09-01)

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Combined deficiencies of endosomal ganglioside neuraminidases 3 and 4 in mice cause lysosomal GM3 gangliosidosis
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Combined deficiencies of endosomal ganglioside neuraminidases 3 and 4 in mice cause lysosomal GM3 gangliosidosis
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Reduced sphingolipid hydrolase activities, substrate accumulation and ganglioside decline in Parkinson’s disease
حسب: Huebecker, M, وآخرون
منشور في: (2019)

Glycosphingolipid storage leads to the enhanced degradation of the B cell receptor in Sandhoff disease mice.
حسب: te Vruchte, D, وآخرون
منشور في: (2010)

CREB5 hypermethylation involved in the ganglioside GM1 therapy of Parkinson’s disease
حسب: Rui Wang, وآخرون
منشور في: (2023-05-01)

Enhanced Susceptibility to Chemoconvulsant-Induced Seizures in Ganglioside GM3 Synthase Knockout Mice
حسب: Fu-Lei Tang, وآخرون
منشور في: (2020-07-01)

The Key Role of GM1 Ganglioside in Parkinson’s Disease
حسب: Suman Chowdhury, وآخرون
منشور في: (2022-01-01)

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Reduced sphingolipid hydrolase activities, substrate accumulation and ganglioside decline in Parkinson’s disease
حسب: Mylene Huebecker, وآخرون
منشور في: (2019-11-01)

Sialidase NEU3 action on GM1 ganglioside is neuroprotective in GM1 gangliosidosis
حسب: Maria L. Allende, وآخرون
منشور في: (2023-12-01)

Intraventricular Sialidase Administration Enhances GM1 Ganglioside Expression and Is Partially Neuroprotective in a Mouse Model of Parkinson's Disease.
حسب: Jay S Schneider, وآخرون
منشور في: (2015-01-01)

Infantile Sandhoff's disease
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منشور في: (2009-08-01)