Up-regulation of utrophin alleviates the dystrophic phenotype in the mdx mouse heart

Up-regulation of utrophin alleviates the dystrophic phenotype in the mdx mouse heart

Detalles Bibliográficos
Autores principales:	Sang, E, Bia, B, Tinsley, J, Davies, K, Clarke, K
Formato:	Journal article
Publicado:	2000

Ejemplares similares

Non-toxic ubiquitous overexpression of utrophin in the mdx mouse.
por: Fisher, R, et al.
Publicado: (2000)

Non-toxic ubiquitous over-expression of utrophin in the mdx mouse.
por: Fisher, R, et al.
Publicado: (2001)

Prevention of the dystrophic phenotype in dystrophin/utrophin-deficient muscle following adenovirus-mediated transfer of a utrophin minigene.
por: Wakefield, P, et al.
Publicado: (2000)

Daily treatment with SMTC1100, a novel small molecule utrophin upregulator, dramatically reduces the dystrophic symptoms in the mdx mouse.
por: Tinsley, J, et al.
Publicado: (2011)

A-utrophin up-regulation in mdx skeletal muscle is independent of regeneration.
por: Weir, A, et al.
Publicado: (2004)

Increased susceptibility of the dystrophic mdx mouse heart to ischemic and hypoxic injuries
por: Zhang, W, et al.
Publicado: (2005)

Daily treatment with SMTC1100, a novel small molecule utrophin upregulator, dramatically reduces the dystrophic symptoms in the mdx mouse.
por: Jonathon M Tinsley, et al.
Publicado: (2011-05-01)

Chronic Dosing with Membrane Sealant Poloxamer 188 NF Improves Respiratory Dysfunction in Dystrophic Mdx and Mdx/Utrophin-/- Mice.
por: Bruce E Markham, et al.
Publicado: (2015-01-01)

A- and B-utrophin have different expression patterns and are differentially up-regulated in mdx muscle.
por: Weir, A, et al.
Publicado: (2002)

Abnormal cardiac morphology, function and energy metabolism in the dystrophic mdx mouse: an MRI and MRS study.
por: Zhang, W, et al.
Publicado: (2008)

Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system.
por: Squire, S, et al.
Publicado: (2002)

Heregulin ameliorates the dystrophic phenotype in mdx mice.
por: Krag, T, et al.
Publicado: (2004)

T-cell-dependent fibrosis in the mdx dystrophic mouse.
por: Morrison, J, et al.
Publicado: (2000)

Decrease in prosaposin in the Dystrophic mdx mouse brain.
por: Hui-Ling Gao, et al.
Publicado: (2013-01-01)

Utrophin influences mitochondrial pathology and oxidative stress in dystrophic muscle
por: Kennedy, T, et al.
Publicado: (2017)

l-arginine improves dystrophic phenotype in mdx mice
por: Vincent Voisin, et al.
Publicado: (2005-10-01)

Muscle structure influences utrophin expression in mdx mice.
por: Glen B Banks, et al.
Publicado: (2014-06-01)

Dystrophic phenotype improvement in the diaphragm muscle of mdx mice by diacerhein.
por: Rafael Dias Mâncio, et al.
Publicado: (2017-01-01)

Utrophin influences mitochondrial pathology and oxidative stress in dystrophic muscle
por: Tahnee L. Kennedy, et al.
Publicado: (2017-10-01)

Microarray analysis of mdx mice expressing high levels of utrophin: therapeutic implications for dystrophin deficiency.
por: Baban, D, et al.
Publicado: (2008)

Dystrophic phenotype of canine X-linked muscular dystrophy is mitigated by adenovirus-mediated utrophin gene transfer.
por: Cerletti, M, et al.
Publicado: (2003)

Regulation of utrophin in transgenic mice.
por: Davies, K
Publicado: (2005)

Metabolic profiles of dystrophin and utrophin expression in mouse models of Duchenne muscular dystrophy.
por: Griffin, J, et al.
Publicado: (2002)

Cardioprotective Effect of Whole Body Periodic Acceleration in Dystrophic Phenotype mdx Rodent
por: Arkady Uryash, et al.
Publicado: (2021-05-01)

Functional amounts of dystrophin produced by skipping the mutated exon in the mdx dystrophic mouse.
por: Lu, Q, et al.
Publicado: (2003)

Functional improvement of dystrophic muscle by repression of utrophin: let-7c interaction.
por: Manoj K Mishra, et al.
Publicado: (2017-01-01)

Utrophin luciferase knock-in mouse model for in vivo assessment of drug efficacy in preclinical trials for utrophin upregulation
por: Fairclough, R, et al.
Publicado: (2010)

Increased mitochondrial uncoupling protein 3 is associated with the cardiomyopathy in the dystrophic mouse heart
por: Zhang, W, et al.
Publicado: (2006)

Micro-utrophin improves cardiac and skeletal muscle function of severely affected D2/mdx mice
por: Kennedy, T, et al.
Publicado: (2018)

Utrophin in the therapy of Duchenne Muscular Dystrophy
por: Potter, A, et al.
Publicado: (2006)

Choline administration attenuates aspects of the dystrophic pathology in mdx mice
por: Francesca M. Alves, et al.
Publicado: (2019-04-01)

Use of antisense-mediated exon skipping to generate dystrophin in muscles of the mdx dystrophic mouse
por: Lu, Q, et al.
Publicado: (2004)

Confirmation by immunogold labeling that utrophin is localised to the normal position of dystrophin in dystrophin-negative transgenic mouse muscle
por: Cullen, M, et al.
Publicado: (2001)

Erythropoietin reduces the expression of myostatin in mdx dystrophic mice
por: D. Feder, et al.
Publicado: (2014-11-01)

Prevention of dystrophic pathology in severely affected dystrophin/utrophin-deficient mice by morpholino-oligomer-mediated exon-skipping.
por: Goyenvalle, A, et al.
Publicado: (2010)

Utrophin up-regulation by an artificial transcription factor in transgenic mice
por: Mattei, E, et al.
Publicado: (2007)

Testing of SHIRPA, a mouse phenotypic assessment protocol, on Dmd(mdx) and Dmd(mdx3cv) dystrophin-deficient mice.
por: Rafael, J, et al.
Publicado: (2000)

Mutation types and aging differently affect revertant fiber expansion in dystrophic mdx and mdx52 mice.
por: Yusuke Echigoya, et al.
Publicado: (2013-01-01)

Proteome Profiling of the Dystrophic <i>mdx</i> Mice Diaphragm
por: Olga Mucha, et al.
Publicado: (2023-11-01)

Dysfunctional muscle and liver glycogen metabolism in mdx dystrophic mice.
por: David I Stapleton, et al.
Publicado: (2014-01-01)