Congenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis?
Congenital bilateral perisylvian syndrome (CBPS) is a syndrome of cortical malformation characterized by faciopharyngoglossomasticatory diplegia. We report on two cases of CBPS with associated esophageal malformations and a poor mental and motor development. The association of CBPS and esophageal ma...
| Main Authors: | , , , |
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| Format: | Journal article |
| Language: | English |
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2000
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| _version_ | 1826296291531948032 |
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| author | Küker, W Friese, S Riethmüller, J Krägeloh-Mann, I |
| author_facet | Küker, W Friese, S Riethmüller, J Krägeloh-Mann, I |
| author_sort | Küker, W |
| collection | OXFORD |
| description | Congenital bilateral perisylvian syndrome (CBPS) is a syndrome of cortical malformation characterized by faciopharyngoglossomasticatory diplegia. We report on two cases of CBPS with associated esophageal malformations and a poor mental and motor development. The association of CBPS and esophageal malformations may indicate a subgroup of patients with a very early prenatal injury, characterised by a bad prognosis due to severe cortical disorganization. However, it can not be excluded that the association of CBPS and esophageal malformation is purely coincidental. |
| first_indexed | 2024-03-07T04:14:05Z |
| format | Journal article |
| id | oxford-uuid:c8d146fa-fa9b-4a17-af78-bcbe8d1c27b5 |
| institution | University of Oxford |
| language | English |
| last_indexed | 2024-03-07T04:14:05Z |
| publishDate | 2000 |
| record_format | dspace |
| spelling | oxford-uuid:c8d146fa-fa9b-4a17-af78-bcbe8d1c27b52022-03-27T06:54:44ZCongenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis?Journal articlehttp://purl.org/coar/resource_type/c_dcae04bcuuid:c8d146fa-fa9b-4a17-af78-bcbe8d1c27b5EnglishSymplectic Elements at Oxford2000Küker, WFriese, SRiethmüller, JKrägeloh-Mann, ICongenital bilateral perisylvian syndrome (CBPS) is a syndrome of cortical malformation characterized by faciopharyngoglossomasticatory diplegia. We report on two cases of CBPS with associated esophageal malformations and a poor mental and motor development. The association of CBPS and esophageal malformations may indicate a subgroup of patients with a very early prenatal injury, characterised by a bad prognosis due to severe cortical disorganization. However, it can not be excluded that the association of CBPS and esophageal malformation is purely coincidental. |
| spellingShingle | Küker, W Friese, S Riethmüller, J Krägeloh-Mann, I Congenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis? |
| title | Congenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis? |
| title_full | Congenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis? |
| title_fullStr | Congenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis? |
| title_full_unstemmed | Congenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis? |
| title_short | Congenital bilateral perisylvian syndrome (CBPS): do concomitant esophageal malformations indicate a poor prognosis? |
| title_sort | congenital bilateral perisylvian syndrome cbps do concomitant esophageal malformations indicate a poor prognosis |
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