Diaphragm rescue alone prevents heart dysfunction in dystrophic mice.

Diaphragm rescue alone prevents heart dysfunction in dystrophic mice.

Duchenne muscular dystrophy (DMD) is an X-linked recessive disease caused, in most cases, by the complete absence of the 427 kDa cytoskeletal protein, dystrophin. There is no effective treatment, and affected individuals die from respiratory failure and cardiomyopathy by age 30. Here, we investigate...

書誌詳細
主要な著者:	Crisp, A, Yin, H, Goyenvalle, A, Betts, C, Moulton, H, Seow, Y, Babbs, A, Merritt, T, Saleh, A, Gait, M, Stuckey, D, Clarke, K, Davies, K, Wood, M
フォーマット:	Journal article
言語:	English
出版事項:	2011

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