New developments in treating glycosphingolipid storage diseases.

New developments in treating glycosphingolipid storage diseases.

Bibliográfalaš dieđut
Váldodahkkit:	Platt, F, Jeyakumar, M, Andersson, U, Dwek, R, Butters, T
Materiálatiipa:	Journal article
Giella:	English
Almmustuhtton:	2005

Geahča maid

Glycosphingolipid lysosomal storage diseases: therapy and pathogenesis.
Dahkki: Jeyakumar, M, et al.
Almmustuhtton: (2002)

New therapeutics for the treatment of glycosphingolipid lysosomal storage diseases.
Dahkki: Butters, T, et al.
Almmustuhtton: (2003)

Inhibition of glycosphingolipid biosynthesis: application to lysosomal storage disorders.
Dahkki: Butters, T, et al.
Almmustuhtton: (2000)

Substrate deprivation: a new therapeutic approach for the glycosphingolipid lysosomal storage diseases.
Dahkki: Platt, F, et al.
Almmustuhtton: (2000)

N-butyldeoxygalactonojirimycin: a more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo.
Dahkki: Andersson, U, et al.
Almmustuhtton: (2000)

Lysosomal storage of oligosaccharide and glycosphingolipid in imino sugar treated cells.
Dahkki: Boomkamp, S, et al.
Almmustuhtton: (2010)

Storage solutions: treating lysosomal disorders of the brain.
Dahkki: Jeyakumar, M, et al.
Almmustuhtton: (2005)

Pharmacological impairment of acrosome formation and sperm head morphogenesis reveals essential role of glycosphingolipids in spermiogenesis
Dahkki: van der Spoel, A, et al.
Almmustuhtton: (2002)

Glycosphingolipid profiling of tissues from mouse models of human lysosomal storage disorders
Dahkki: Priestman, D, et al.
Almmustuhtton: (2008)

Impaired selection of invariant natural killer T cells in diverse mouse models of glycosphingolipid lysosomal storage diseases
Dahkki: Silk, J, et al.
Almmustuhtton: (2005)

Impaired selection of invariant natural killer T cells in diverse mouse models of glycosphingolipid lysosomal storage diseases.
Dahkki: Gadola, S, et al.
Almmustuhtton: (2006)

Cellular effects of deoxynojirimycin analogues: uptake, retention and inhibition of glycosphingolipid biosynthesis.
Dahkki: Mellor, H, et al.
Almmustuhtton: (2004)

Modulation of THP-1 macrophage and cholesterol-loaded foam cell apolipoprotein E levels by glycosphingolipids.
Dahkki: Garner, B, et al.
Almmustuhtton: (2002)

Substrate reduction therapy for glycosphingolipid storage disorders.
Dahkki: Lachmann, R, et al.
Almmustuhtton: (2001)

Molecular requirements of imino sugars for the selective control of N-linked glycosylation and glycosphingolipid biosynthesis
Dahkki: Butters, T, et al.
Almmustuhtton: (2000)

ALTERED AUTOPHAGY AND APP METABOLISM IN GLYCOSPHINGOLIPID STORAGE DISEASES
Dahkki: Boland, B, et al.
Almmustuhtton: (2011)

Glycosphingolipid disorders of the brain.
Dahkki: Boomkamp, S, et al.
Almmustuhtton: (2008)

Substrate reduction therapy in mouse models of the glycosphingolipidoses.
Dahkki: Platt, F, et al.
Almmustuhtton: (2003)

Introduction: Glycosphingolipids in cell biology and disease.
Dahkki: Sillence, D, et al.
Almmustuhtton: (2004)

Improved outcome of N-butyldeoxygalactonojirimycin-mediated substrate reduction therapy in a mouse model of Sandhoff disease.
Dahkki: Andersson, U, et al.
Almmustuhtton: (2004)

Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling.
Dahkki: Neville, D, et al.
Almmustuhtton: (2004)

Therapeutic applications of imino sugars in lysosomal storage disorders.
Dahkki: Butters, T, et al.
Almmustuhtton: (2003)

Iminosugar inhibitors for treating the lysosomal glycosphingolipidoses
Dahkki: Butters, T, et al.
Almmustuhtton: (2005)

Accumulation of glycosphingolipids in Niemann-Pick C disease disrupts endosomal transport.
Dahkki: te Vruchte, D, et al.
Almmustuhtton: (2004)

Imino sugar inhibitors for treating the lysosomal glycosphingolipidoses.
Dahkki: Butters, T, et al.
Almmustuhtton: (2005)

Glycosphingolipid storage leads to the enhanced degradation of the B cell receptor in Sandhoff disease mice.
Dahkki: te Vruchte, D, et al.
Almmustuhtton: (2010)

Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice.
Dahkki: Garner, B, et al.
Almmustuhtton: (2002)

Glycosphingolipids in endocytic membrane transport.
Dahkki: Sillence, D, et al.
Almmustuhtton: (2004)

Diverse endogenous antigens for mouse NKT cells: self-antigens that are not glycosphingolipids.
Dahkki: Pei, B, et al.
Almmustuhtton: (2011)

The apo E gene knockout mouse as a model to study the potential atherogenic properties of glycosphingolipids
Dahkki: Garner, B, et al.
Almmustuhtton: (2003)

Apoptotic modification of glycosphingolipids of human granulocytes
Dahkki: A. M. Tomin, et al.
Almmustuhtton: (2012-09-01)

The development and use of small molecule inhibitors of glycosphingolipid metabolism for lysosomal storage diseases
Dahkki: James A. Shayman, et al.
Almmustuhtton: (2014-07-01)

Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice
Dahkki: Brett Garner, et al.
Almmustuhtton: (2002-02-01)

Glycosphingolipid metabolism and its role in ageing and Parkinson’s disease
Dahkki: Wallom, K-L, et al.
Almmustuhtton: (2021)

Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy.
Dahkki: Platt, F, et al.
Almmustuhtton: (2001)

Inhibition of glycogen breakdown by imino sugars in vitro and in vivo.
Dahkki: Andersson, U, et al.
Almmustuhtton: (2004)

Small-molecule therapeutics for the treatment of glycolipid lysosomal storage disorders.
Dahkki: Butters, T, et al.
Almmustuhtton: (2003)

Activation state and intracellular trafficking contribute to the repertoire of endogenous glycosphingolipids presented by CD1d [corrected].
Dahkki: Muindi, K, et al.
Almmustuhtton: (2010)

Glycosphingolipid synthesis inhibition limits osteoclast activation and myeloma bone disease
Dahkki: Ersek, A, et al.
Almmustuhtton: (2015)

Iminosugars and methods of treating viral diseases
Dahkki: Ramstedt, U, et al.
Almmustuhtton: (2011)