Primary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency

We report the updated classification of primary immunodeficiency diseases, compiled by the ad hoc Expert Committee of the International Union of Immunological Societies. As compared to the previous edition, more than 15 novel disease entities have been added in the updated version. For each disorder...

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Main Authors: Al-Herz, W, Bousfiha, A, Casanova, J, Chapel, H, Conley, M, Cunningham-Rundles, C, Etzioni, A, Fischer, A, Franco, J, Geha, R, Hammarström, L, Nonoyama, S, Notarangelo, L, Ochs, H, Puck, J, Roifman, C, Seger, R, Tang, M
Format: Journal article
Language:English
Published: 2011
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author Al-Herz, W
Bousfiha, A
Casanova, J
Chapel, H
Conley, M
Cunningham-Rundles, C
Etzioni, A
Fischer, A
Franco, J
Geha, R
Hammarström, L
Nonoyama, S
Notarangelo, L
Ochs, H
Puck, J
Roifman, C
Seger, R
Tang, M
author_facet Al-Herz, W
Bousfiha, A
Casanova, J
Chapel, H
Conley, M
Cunningham-Rundles, C
Etzioni, A
Fischer, A
Franco, J
Geha, R
Hammarström, L
Nonoyama, S
Notarangelo, L
Ochs, H
Puck, J
Roifman, C
Seger, R
Tang, M
author_sort Al-Herz, W
collection OXFORD
description We report the updated classification of primary immunodeficiency diseases, compiled by the ad hoc Expert Committee of the International Union of Immunological Societies. As compared to the previous edition, more than 15 novel disease entities have been added in the updated version. For each disorders, the key clinical and laboratory features are provided. This updated classification is meant to help in the diagnostic approach to patients with these diseases. © 2011 Al-Herz, Bous-?ha, Casanova, Chapel, Conley, Cunningham-Rundles, Etzioni,Fischer, Franco, Geha, Hammarström, Nonoyama, Notarangelo, Ochs, Puck, Roifman, Seger and Tang.
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spelling oxford-uuid:ff6e350e-2ab3-4b35-87ef-d996673c09542022-03-27T13:44:55ZPrimary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary ImmunodeficiencyJournal articlehttp://purl.org/coar/resource_type/c_dcae04bcuuid:ff6e350e-2ab3-4b35-87ef-d996673c0954EnglishSymplectic Elements at Oxford2011Al-Herz, WBousfiha, ACasanova, JChapel, HConley, MCunningham-Rundles, CEtzioni, AFischer, AFranco, JGeha, RHammarström, LNonoyama, SNotarangelo, LOchs, HPuck, JRoifman, CSeger, RTang, MWe report the updated classification of primary immunodeficiency diseases, compiled by the ad hoc Expert Committee of the International Union of Immunological Societies. As compared to the previous edition, more than 15 novel disease entities have been added in the updated version. For each disorders, the key clinical and laboratory features are provided. This updated classification is meant to help in the diagnostic approach to patients with these diseases. © 2011 Al-Herz, Bous-?ha, Casanova, Chapel, Conley, Cunningham-Rundles, Etzioni,Fischer, Franco, Geha, Hammarström, Nonoyama, Notarangelo, Ochs, Puck, Roifman, Seger and Tang.
spellingShingle Al-Herz, W
Bousfiha, A
Casanova, J
Chapel, H
Conley, M
Cunningham-Rundles, C
Etzioni, A
Fischer, A
Franco, J
Geha, R
Hammarström, L
Nonoyama, S
Notarangelo, L
Ochs, H
Puck, J
Roifman, C
Seger, R
Tang, M
Primary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency
title Primary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency
title_full Primary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency
title_fullStr Primary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency
title_full_unstemmed Primary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency
title_short Primary immunodeficiency diseases: An update on the classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency
title_sort primary immunodeficiency diseases an update on the classification from the international union of immunological societies expert committee for primary immunodeficiency
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