Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension

Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital heart disease and transient myeloproliferative...

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Main Authors: Zahari, Norazah, Sirisani, Joyce Darshinee Dom
Format: Article
Published: Malaysian Medical Association 2018
Subjects:
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author Zahari, Norazah
Sirisani, Joyce Darshinee Dom
author_facet Zahari, Norazah
Sirisani, Joyce Darshinee Dom
author_sort Zahari, Norazah
collection UM
description Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital heart disease and transient myeloproliferative leukaemia. This case-report aims to improve awareness among physicians and sonographers of this disease and the importance of pulmonary vein assessment in congenital heart disease with unexplained pulmonary hypertension.
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spelling um.eprints-202192019-01-30T02:15:52Z http://eprints.um.edu.my/20219/ Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension Zahari, Norazah Sirisani, Joyce Darshinee Dom R Medicine RJ Pediatrics Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital heart disease and transient myeloproliferative leukaemia. This case-report aims to improve awareness among physicians and sonographers of this disease and the importance of pulmonary vein assessment in congenital heart disease with unexplained pulmonary hypertension. Malaysian Medical Association 2018 Article PeerReviewed Zahari, Norazah and Sirisani, Joyce Darshinee Dom (2018) Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension. Medical Journal of Malaysia, 73 (2). pp. 119-120. ISSN 0300-5283, http://www.e-mjm.org/2018/v73n2/pulmonary-hypertension.pdf
spellingShingle R Medicine
RJ Pediatrics
Zahari, Norazah
Sirisani, Joyce Darshinee Dom
Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension
title Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension
title_full Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension
title_fullStr Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension
title_full_unstemmed Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension
title_short Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension
title_sort progressive pulmonary vein stenosis in down syndrome infant a rare cause of pulmonary hypertension
topic R Medicine
RJ Pediatrics
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