Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension
Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital heart disease and transient myeloproliferative...
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Malaysian Medical Association
2018
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author | Zahari, Norazah Sirisani, Joyce Darshinee Dom |
author_facet | Zahari, Norazah Sirisani, Joyce Darshinee Dom |
author_sort | Zahari, Norazah |
collection | UM |
description | Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital heart disease and transient myeloproliferative leukaemia. This case-report aims to improve awareness among physicians and sonographers of this disease and the importance of pulmonary vein assessment in congenital heart disease with unexplained pulmonary hypertension. |
first_indexed | 2024-03-06T05:50:34Z |
format | Article |
id | um.eprints-20219 |
institution | Universiti Malaya |
last_indexed | 2024-03-06T05:50:34Z |
publishDate | 2018 |
publisher | Malaysian Medical Association |
record_format | dspace |
spelling | um.eprints-202192019-01-30T02:15:52Z http://eprints.um.edu.my/20219/ Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension Zahari, Norazah Sirisani, Joyce Darshinee Dom R Medicine RJ Pediatrics Pulmonary veins stenosis in a Down Syndrome infant with normal connection pulmonary vein is rare and precise incidence of this disease is unknown. We report a case of progressive multiple pulmonary vein stenosis in a Down Syndrome infant with congenital heart disease and transient myeloproliferative leukaemia. This case-report aims to improve awareness among physicians and sonographers of this disease and the importance of pulmonary vein assessment in congenital heart disease with unexplained pulmonary hypertension. Malaysian Medical Association 2018 Article PeerReviewed Zahari, Norazah and Sirisani, Joyce Darshinee Dom (2018) Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension. Medical Journal of Malaysia, 73 (2). pp. 119-120. ISSN 0300-5283, http://www.e-mjm.org/2018/v73n2/pulmonary-hypertension.pdf |
spellingShingle | R Medicine RJ Pediatrics Zahari, Norazah Sirisani, Joyce Darshinee Dom Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension |
title | Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension |
title_full | Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension |
title_fullStr | Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension |
title_full_unstemmed | Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension |
title_short | Progressive pulmonary vein stenosis in down syndrome infant: A rare cause of pulmonary hypertension |
title_sort | progressive pulmonary vein stenosis in down syndrome infant a rare cause of pulmonary hypertension |
topic | R Medicine RJ Pediatrics |
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