Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach
Primary optic nerve sheath meningioma is generally a benign tumor. In rare instances, however, the growth rate and intraocular and intracranial extensions can be highly aggressive, especially in children, leading to poor prognosis. Here, we reported a case of a 24-year-old woman who presented with l...
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| Format: | Article |
| Language: | English English |
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Faculty of Medicine, Universitas Indonesia
2023
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| Online Access: | https://eprints.ums.edu.my/id/eprint/38239/1/ABSTRACT.pdf https://eprints.ums.edu.my/id/eprint/38239/2/FULL%20TEXT.pdf |
| _version_ | 1796912049553408000 |
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| author | Sylves Patrick Yeap Boon Tat Muhamad Zarif Mohd Amin Maftuhim Addenan Shuaibah Ab.Ghani Hanida Hanafi |
| author_facet | Sylves Patrick Yeap Boon Tat Muhamad Zarif Mohd Amin Maftuhim Addenan Shuaibah Ab.Ghani Hanida Hanafi |
| author_sort | Sylves Patrick |
| collection | UMS |
| description | Primary optic nerve sheath meningioma is generally a benign tumor. In rare instances, however, the growth rate and intraocular and intracranial extensions can be highly aggressive, especially in children, leading to poor prognosis. Here, we reported a case of a 24-year-old woman who presented with left eye swelling for 3 years. This was associated with blurred vision, retrobulbar pain, and redness. On examination, the left eye was severely proptosed with complete ophthalmoplegia. Magnetic resonance imaging showed an extensive tumor occupying the whole left orbital cavity with a disfigured eyeball. However, no intracranial extension was observed. Interestingly, complete surgical excision was feasible via transconjunctival anterior orbitotomy without bone removal. The histopathological examination confirmed the diagnosis of optic nerve sheath meningioma. Adjunct radiotherapy was given. On a follow-up after 2 years, left enophthalmos with esotropia was observed. |
| first_indexed | 2024-03-06T03:27:46Z |
| format | Article |
| id | ums.eprints-38239 |
| institution | Universiti Malaysia Sabah |
| language | English English |
| last_indexed | 2024-03-06T03:27:46Z |
| publishDate | 2023 |
| publisher | Faculty of Medicine, Universitas Indonesia |
| record_format | dspace |
| spelling | ums.eprints-382392024-02-15T02:29:57Z https://eprints.ums.edu.my/id/eprint/38239/ Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach Sylves Patrick Yeap Boon Tat Muhamad Zarif Mohd Amin Maftuhim Addenan Shuaibah Ab.Ghani Hanida Hanafi RD1-811 Surgery RE1-994 Ophthalmology Primary optic nerve sheath meningioma is generally a benign tumor. In rare instances, however, the growth rate and intraocular and intracranial extensions can be highly aggressive, especially in children, leading to poor prognosis. Here, we reported a case of a 24-year-old woman who presented with left eye swelling for 3 years. This was associated with blurred vision, retrobulbar pain, and redness. On examination, the left eye was severely proptosed with complete ophthalmoplegia. Magnetic resonance imaging showed an extensive tumor occupying the whole left orbital cavity with a disfigured eyeball. However, no intracranial extension was observed. Interestingly, complete surgical excision was feasible via transconjunctival anterior orbitotomy without bone removal. The histopathological examination confirmed the diagnosis of optic nerve sheath meningioma. Adjunct radiotherapy was given. On a follow-up after 2 years, left enophthalmos with esotropia was observed. Faculty of Medicine, Universitas Indonesia 2023 Article NonPeerReviewed text en https://eprints.ums.edu.my/id/eprint/38239/1/ABSTRACT.pdf text en https://eprints.ums.edu.my/id/eprint/38239/2/FULL%20TEXT.pdf Sylves Patrick and Yeap Boon Tat and Muhamad Zarif Mohd Amin and Maftuhim Addenan and Shuaibah Ab.Ghani and Hanida Hanafi (2023) Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach. Medical Journal of Indonesia, 32 (3). pp. 1-4. ISSN 0853-1773 https://doi.org/10.13181/mji.cr.236936 |
| spellingShingle | RD1-811 Surgery RE1-994 Ophthalmology Sylves Patrick Yeap Boon Tat Muhamad Zarif Mohd Amin Maftuhim Addenan Shuaibah Ab.Ghani Hanida Hanafi Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach |
| title | Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach |
| title_full | Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach |
| title_fullStr | Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach |
| title_full_unstemmed | Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach |
| title_short | Atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis: an alternative surgical approach |
| title_sort | atypical orbital primary optic nerve sheath meningioma with severe disfiguring proptosis an alternative surgical approach |
| topic | RD1-811 Surgery RE1-994 Ophthalmology |
| url | https://eprints.ums.edu.my/id/eprint/38239/1/ABSTRACT.pdf https://eprints.ums.edu.my/id/eprint/38239/2/FULL%20TEXT.pdf |
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