A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
Bickerstaff Brainstem Encephalitis (BBE) is a post-infectious immune disorder. It is rare, yet the most severe variant of Guillain-Barre Syndrome (GBS) in terms of initial presentation. Moreover, the coexistence of BBE and Acute Lymphoblastic Leukaemia (ALL) is distinctly uncommon. We report a case...
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Format: | Article |
Language: | English |
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Lahore Medical & Dental College
2014
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Online Access: | http://psasir.upm.edu.my/id/eprint/36123/1/A%20case%20of%20Bickerstaff%20brainstem%20encephalitis%20and%20acute%20lymphoblastic%20leukaemia.pdf |
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author | Hashim, Hasriza Sulaiman Sahari, Narisa Mohd Sazlly Lim, Sazlyna Hasan, Shariful Hoo, Fan Kee |
author_facet | Hashim, Hasriza Sulaiman Sahari, Narisa Mohd Sazlly Lim, Sazlyna Hasan, Shariful Hoo, Fan Kee |
author_sort | Hashim, Hasriza |
collection | UPM |
description | Bickerstaff Brainstem Encephalitis (BBE) is a post-infectious immune disorder. It is rare, yet the most severe variant of Guillain-Barre Syndrome (GBS) in terms of initial presentation. Moreover, the coexistence of BBE and Acute Lymphoblastic Leukaemia (ALL) is distinctly uncommon. We report a case of a patient with a background history of Precursor B cell Acute Lymphoblastic Leukaemia (pre B ALL) presented with a mixture of peripheral and central nervous system involvement with cortical, subcortical and cerebellar lesions on brain magnetic resonance imaging (MRI), and was eventually diagnosed with BBE. In this case, we illustrate the complexity in diagnosing BBE, a rare variant of GBS due to atypical presentation. |
first_indexed | 2024-03-06T08:34:23Z |
format | Article |
id | upm.eprints-36123 |
institution | Universiti Putra Malaysia |
language | English |
last_indexed | 2024-03-06T08:34:23Z |
publishDate | 2014 |
publisher | Lahore Medical & Dental College |
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spelling | upm.eprints-361232015-09-10T06:45:41Z http://psasir.upm.edu.my/id/eprint/36123/ A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia Hashim, Hasriza Sulaiman Sahari, Narisa Mohd Sazlly Lim, Sazlyna Hasan, Shariful Hoo, Fan Kee Bickerstaff Brainstem Encephalitis (BBE) is a post-infectious immune disorder. It is rare, yet the most severe variant of Guillain-Barre Syndrome (GBS) in terms of initial presentation. Moreover, the coexistence of BBE and Acute Lymphoblastic Leukaemia (ALL) is distinctly uncommon. We report a case of a patient with a background history of Precursor B cell Acute Lymphoblastic Leukaemia (pre B ALL) presented with a mixture of peripheral and central nervous system involvement with cortical, subcortical and cerebellar lesions on brain magnetic resonance imaging (MRI), and was eventually diagnosed with BBE. In this case, we illustrate the complexity in diagnosing BBE, a rare variant of GBS due to atypical presentation. Lahore Medical & Dental College 2014 Article PeerReviewed application/pdf en http://psasir.upm.edu.my/id/eprint/36123/1/A%20case%20of%20Bickerstaff%20brainstem%20encephalitis%20and%20acute%20lymphoblastic%20leukaemia.pdf Hashim, Hasriza and Sulaiman Sahari, Narisa and Mohd Sazlly Lim, Sazlyna and Hasan, Shariful and Hoo, Fan Kee (2014) A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia. Pakistan Journal of Medical and Health Sciences, 8 (4). pp. 1125-1127. ISSN 1996-7195 http://pjmhsonline.com/OctDec2014/ |
spellingShingle | Hashim, Hasriza Sulaiman Sahari, Narisa Mohd Sazlly Lim, Sazlyna Hasan, Shariful Hoo, Fan Kee A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia |
title | A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia |
title_full | A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia |
title_fullStr | A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia |
title_full_unstemmed | A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia |
title_short | A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia |
title_sort | case of bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia |
url | http://psasir.upm.edu.my/id/eprint/36123/1/A%20case%20of%20Bickerstaff%20brainstem%20encephalitis%20and%20acute%20lymphoblastic%20leukaemia.pdf |
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