A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia

Bickerstaff Brainstem Encephalitis (BBE) is a post-infectious immune disorder. It is rare, yet the most severe variant of Guillain-Barre Syndrome (GBS) in terms of initial presentation. Moreover, the coexistence of BBE and Acute Lymphoblastic Leukaemia (ALL) is distinctly uncommon. We report a case...

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Main Authors: Hashim, Hasriza, Sulaiman Sahari, Narisa, Mohd Sazlly Lim, Sazlyna, Hasan, Shariful, Hoo, Fan Kee
Format: Article
Language:English
Published: Lahore Medical & Dental College 2014
Online Access:http://psasir.upm.edu.my/id/eprint/36123/1/A%20case%20of%20Bickerstaff%20brainstem%20encephalitis%20and%20acute%20lymphoblastic%20leukaemia.pdf
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author Hashim, Hasriza
Sulaiman Sahari, Narisa
Mohd Sazlly Lim, Sazlyna
Hasan, Shariful
Hoo, Fan Kee
author_facet Hashim, Hasriza
Sulaiman Sahari, Narisa
Mohd Sazlly Lim, Sazlyna
Hasan, Shariful
Hoo, Fan Kee
author_sort Hashim, Hasriza
collection UPM
description Bickerstaff Brainstem Encephalitis (BBE) is a post-infectious immune disorder. It is rare, yet the most severe variant of Guillain-Barre Syndrome (GBS) in terms of initial presentation. Moreover, the coexistence of BBE and Acute Lymphoblastic Leukaemia (ALL) is distinctly uncommon. We report a case of a patient with a background history of Precursor B cell Acute Lymphoblastic Leukaemia (pre B ALL) presented with a mixture of peripheral and central nervous system involvement with cortical, subcortical and cerebellar lesions on brain magnetic resonance imaging (MRI), and was eventually diagnosed with BBE. In this case, we illustrate the complexity in diagnosing BBE, a rare variant of GBS due to atypical presentation.
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spelling upm.eprints-361232015-09-10T06:45:41Z http://psasir.upm.edu.my/id/eprint/36123/ A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia Hashim, Hasriza Sulaiman Sahari, Narisa Mohd Sazlly Lim, Sazlyna Hasan, Shariful Hoo, Fan Kee Bickerstaff Brainstem Encephalitis (BBE) is a post-infectious immune disorder. It is rare, yet the most severe variant of Guillain-Barre Syndrome (GBS) in terms of initial presentation. Moreover, the coexistence of BBE and Acute Lymphoblastic Leukaemia (ALL) is distinctly uncommon. We report a case of a patient with a background history of Precursor B cell Acute Lymphoblastic Leukaemia (pre B ALL) presented with a mixture of peripheral and central nervous system involvement with cortical, subcortical and cerebellar lesions on brain magnetic resonance imaging (MRI), and was eventually diagnosed with BBE. In this case, we illustrate the complexity in diagnosing BBE, a rare variant of GBS due to atypical presentation. Lahore Medical & Dental College 2014 Article PeerReviewed application/pdf en http://psasir.upm.edu.my/id/eprint/36123/1/A%20case%20of%20Bickerstaff%20brainstem%20encephalitis%20and%20acute%20lymphoblastic%20leukaemia.pdf Hashim, Hasriza and Sulaiman Sahari, Narisa and Mohd Sazlly Lim, Sazlyna and Hasan, Shariful and Hoo, Fan Kee (2014) A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia. Pakistan Journal of Medical and Health Sciences, 8 (4). pp. 1125-1127. ISSN 1996-7195 http://pjmhsonline.com/OctDec2014/
spellingShingle Hashim, Hasriza
Sulaiman Sahari, Narisa
Mohd Sazlly Lim, Sazlyna
Hasan, Shariful
Hoo, Fan Kee
A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
title A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
title_full A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
title_fullStr A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
title_full_unstemmed A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
title_short A case of Bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
title_sort case of bickerstaff brainstem encephalitis and acute lymphoblastic leukaemia
url http://psasir.upm.edu.my/id/eprint/36123/1/A%20case%20of%20Bickerstaff%20brainstem%20encephalitis%20and%20acute%20lymphoblastic%20leukaemia.pdf
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