Exome Sequencing Diagnoses X-Linked Moesin-Associated Immunodeficiency in a Primary Immunodeficiency Case by Gabrielle Bradshaw, Robbie R. Lualhati, Cassie L. Albury, Neven Maksemous, Deidre Roos-Araujo, Robert A. Smith, Miles C. Benton, David A. Eccles, Rod A. Lea, Heidi G. Sutherland, Larisa M. Haupt, Lyn R. Griffiths

“…WES trio analysis, data filtering and in silico prediction identified a novel, damaging (SIFT: 0; Polyphen 1; Grantham score: 101) and disease-causing (MutationTaster) single base mutation in the X chromosome (c.511C > T p.Arg171Trp) MSN gene not identified in the UCSC Genome Browser database. …”
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Human influence on growing-period frosts like in early April 2021 in central France by R. Vautard, G. J. van Oldenborgh, R. Bonnet, S. Li, Y. Robin, S. Kew, S. Philip, J.-M. Soubeyroux, B. Dubuisson, N. Viovy, M. Reichstein, F. Otto, I. Garcia de Cortazar-Atauri

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Integrated assessment model diagnostics: key indicators and model evolution by Mathijs Harmsen, Elmar Kriegler, Detlef P van Vuuren, Kaj-Ivar van der Wijst, Gunnar Luderer, Ryna Cui, Olivier Dessens, Laurent Drouet, Johannes Emmerling, Jennifer Faye Morris, Florian Fosse, Dimitris Fragkiadakis, Kostas Fragkiadakis, Panagiotis Fragkos, Oliver Fricko, Shinichiro Fujimori, David Gernaat, Céline Guivarch, Gokul Iyer, Panagiotis Karkatsoulis, Ilkka Keppo, Kimon Keramidas, Alexandre Köberle, Peter Kolp, Volker Krey, Christoph Krüger, Florian Leblanc, Shivika Mittal, Sergey Paltsev, Pedro Rochedo, Bas J van Ruijven, Ronald D Sands, Fuminori Sano, Jessica Strefler, Eveline Vasquez Arroyo, Kenichi Wada, Behnam Zakeri

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<i>TreeSatAI Benchmark Archive</i>: a multi-sensor, multi-label dataset for tree species classification in remote sensing by S. Ahlswede, C. Schulz, C. Gava, P. Helber, B. Bischke, M. Förster, F. Arias, J. Hees, J. Hees, B. Demir, B. Kleinschmit

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The challenge to understand the zoo of particle transport regimes during resonant wave-particle interactions for given survey-mode wave spectra by Oliver Allanson, Oliver Allanson, Oliver Allanson, Donglai Ma, Adnane Osmane, Jay M. Albert, Jacob Bortnik, Clare E. J. Watt, Sandra C. Chapman, Sandra C. Chapman, Sandra C. Chapman, Joseph Spencer, Daniel J. Ratliff, Nigel P. Meredith, Thomas Elsden, Thomas Neukirch, David P. Hartley, Rachel Black, Rachel Black, Nicholas W. Watkins, Nicholas W. Watkins, Sean Elvidge

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Role of zooplankton dynamics for Southern Ocean phytoplankton biomass and global biogeochemical cycles by C. Le Quéré, E. T. Buitenhuis, R. Moriarty, S. Alvain, O. Aumont, L. Bopp, S. Chollet, C. Enright, D. J. Franklin, R. J. Geider, S. P. Harrison, A. G. Hirst, S. Larsen, L. Legendre, T. Platt, I. C. Prentice, R. B. Rivkin, S. Sailley, S. Sathyendranath, N. Stephens, M. Vogt, S. M. Vallina

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Towards near-real-time air pollutant and greenhouse gas emissions: lessons learned from multiple estimates during the COVID-19 pandemic by M. Guevara, H. Petetin, O. Jorba, H. Denier van der Gon, J. Kuenen, I. Super, C. Granier, C. Granier, T. Doumbia, P. Ciais, Z. Liu, R. D. Lamboll, S. Schindlbacher, B. Matthews, C. Pérez García-Pando, C. Pérez García-Pando

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The Manchester Respiratory Activities of Daily Living Questionnaire: Reliability and Validity of the Chinese Version with Pictorial Enhancement by Siu DCH, So CT, Lau CWL, Hui EHM, Fung A, Chan TM, Chan FSF, Chan CKF, Chen WPW, Cheung SHM, Chan KPY, Poon P, Cheung M, Chan C, Tse J, Fung V, Fong KNK

“…Damian Chi Hong Siu,1,2 Chi Tao So,1,3 Cherry Wai Lee Lau,1,4 Eric Hei Man Hui,1,5 Alexandra Fung,1,6 Tak Ming Chan,1,7 Fion Siu Fun Chan,1,3 Catherine Kam Fung Chan,1,8 William Pang Wai Chen,1,9 Sammy Hoo Ming Cheung,1,10 Katherine Pui Yee Chan,1,11 Peter Poon,12 Michael Cheung,12 Cherry Chan,12 Justin Tse,12 Vanessa Fung,12 Kenneth NK Fong12 1Respiratory Sub-Specialty Group, Occupational Therapy Central Organization Committee, Hospital Authority, Hong Kong SAR; 2Occupational Therapy Department, Prince of Wales Hospital, Hospital Authority, Hong Kong SAR; 3Occupational Therapy Department, Princess Margaret Hospital, Hospital Authority, Hong Kong SAR; 4Occupational Therapy Department, Kowloon Hospital, Hospital Authority, Hong Kong SAR; 5Occupational Therapy Department, Grantham Hospital, Hospital Authority, Hong Kong SAR; 6Occupational Therapy Department, Ruttonjee Hospital, Hospital Authority, Hong Kong SAR; 7Occupational Therapy Department, Haven of Hope Hospital, Hospital Authority, Hong Kong SAR; 8Occupational Therapy Department, Wong Tai Sin Hospital, Hospital Authority, Hong Kong SAR; 9Occupational Therapy Department, Tseung Kwan O Hospital, Hospital Authority, Hong Kong SAR; 10Occupational Therapy Department, Tuen Mun Hospital, Hospital Authority, Hong Kong SAR; 11Occupational Therapy Department, Alice Ho Miu Ling Nethersole Hospital, Hospital Authority, Hong Kong SAR; 12Department of Rehabilitation Sciences, The Hong Kong Polytechnic University, Hong Kong SARCorrespondence: Damian Chi Hong SiuOccupational Therapy Department, Hospital Authority, Prince of Wales Hospital, 30-32 Ngan Shing Street, Shatin, New Territories, Hong Kong SAR Email damiansiu@gmail.comBackground: The Manchester Respiratory Activities of Daily Living Questionnaire (MRADLQ) is a valid and reliable tool measuring the functional level of patients with COPD in multidimensional aspects. …”
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The Zero Emissions Commitment Model Intercomparison Project (ZECMIP) contribution to C4MIP: quantifying committed climate changes following zero carbon emissions by C. D. Jones, T. L. Frölicher, T. L. Frölicher, C. Koven, A. H. MacDougall, H. D. Matthews, K. Zickfeld, J. Rogelj, J. Rogelj, K. B. Tokarska, K. B. Tokarska, N. P. Gillett, T. Ilyina, M. Meinshausen, M. Meinshausen, N. Mengis, N. Mengis, R. Séférian, M. Eby, F. A. Burger, F. A. Burger

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A novel approach to detect resistance mechanisms reveals FGR as a factor mediating HDAC inhibitor SAHA resistance in B‐cell lymphoma by Maria Joosten, Sebastian Ginzel, Christian Blex, Dmitri Schmidt, Michael Gombert, Cai Chen, René Martin Linka, Olivia Gräbner, Anika Hain, Burkhard Hirsch, Anke Sommerfeld, Anke Seegebarth, Uschi Gruber, Corinna Maneck, Langhui Zhang, Katharina Stenin, Henrik Dieks, Michael Sefkow, Carsten Münk, Claudia D. Baldus, Ralf Thiele, Arndt Borkhardt, Michael Hummel, Hubert Köster, Ute Fischer, Mathias Dreger, Volkhard Seitz

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Quantitative assessment of fire and vegetation properties in simulations with fire-enabled vegetation models from the Fire Model Intercomparison Project by S. Hantson, S. Hantson, D. I. Kelley, A. Arneth, S. P. Harrison, S. Archibald, D. Bachelet, M. Forrest, T. Hickler, T. Hickler, G. Lasslop, F. Li, S. Mangeon, S. Mangeon, J. R. Melton, L. Nieradzik, S. S. Rabin, I. C. Prentice, T. Sheehan, S. Sitch, L. Teckentrup, L. Teckentrup, A. Voulgarakis, C. Yue

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Detecting the human fingerprint in the summer 2022 western–central European soil drought by D. L. Schumacher, M. Zachariah, F. Otto, C. Barnes, S. Philip, S. Kew, M. Vahlberg, R. Singh, D. Heinrich, J. Arrighi, J. Arrighi, J. Arrighi, M. van Aalst, M. van Aalst, M. van Aalst, M. Hauser, M. Hirschi, V. Bessenbacher, V. Bessenbacher, L. Gudmundsson, H. K. Beaudoing, H. K. Beaudoing, M. Rodell, S. Li, W. Yang, G. A. Vecchi, G. A. Vecchi, L. J. Harrington, F. Lehner, F. Lehner, F. Lehner, G. Balsamo, S. I. Seneviratne

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Negative emissions—Part 1: Research landscape and synthesis by Jan C Minx, William F Lamb, Max W Callaghan, Sabine Fuss, Jérôme Hilaire, Felix Creutzig, Thorben Amann, Tim Beringer, Wagner de Oliveira Garcia, Jens Hartmann, Tarun Khanna, Dominic Lenzi, Gunnar Luderer, Gregory F Nemet, Joeri Rogelj, Pete Smith, Jose Luis Vicente Vicente, Jennifer Wilcox, Maria del Mar Zamora Dominguez

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Reading out Khayyam in light of the circumstances of his time Case Study: Garden City, South of Neyshabour (Shadyakh) by nahid jafari dehkordi

“…An Iranian effort to construct a parody of Paradise/ Ferdows or Grantham of Zoroastrianism has given the holy gardens a great value. …”
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Recent trends and drivers of regional sources and sinks of carbon dioxide by S. Sitch, P. Friedlingstein, N. Gruber, S. D. Jones, G. Murray-Tortarolo, A. Ahlström, S. C. Doney, H. Graven, C. Heinze, C. Huntingford, S. Levis, P. E. Levy, M. Lomas, B. Poulter, N. Viovy, S. Zaehle, N. Zeng, A. Arneth, G. Bonan, L. Bopp, J. G. Canadell, F. Chevallier, P. Ciais, R. Ellis, M. Gloor, P. Peylin, S. L. Piao, C. Le Quéré, B. Smith, Z. Zhu, R. Myneni

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Terrestrial biosphere changes over the last 120 kyr by B. A. A. Hoogakker, R. S. Smith, J. S. Singarayer, R. Marchant, I. C. Prentice, J. R. M. Allen, R. S. Anderson, S. A. Bhagwat, H. Behling, O. Borisova, M. Bush, A. Correa-Metrio, A. de Vernal, J. M. Finch, B. Fréchette, S. Lozano-Garcia, W. D. Gosling, W. Granoszewski, E. C. Grimm, E. Grüger, J. Hanselman, S. P. Harrison, T. R. Hill, B. Huntley, G. Jiménez-Moreno, P. Kershaw, M.-P. Ledru, D. Magri, M. McKenzie, U. Müller, T. Nakagawa, E. Novenko, D. Penny, L. Sadori, L. Scott, J. Stevenson, P. J. Valdes, M. Vandergoes, A. Velichko, C. Whitlock, C. Tzedakis

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One Hundred Priority Questions for the Development of Sustainable Food Systems in Sub-Saharan Africa by Adam J. M. Devenish, Petra Schmitter, Nugun. P. Jellason, Nafeesa Esmail, Nur M. Abdi, Selase K. Adanu, Barbara Adolph, Maha Al-Zu’bi, Amali A. Amali, Jennie Barron, Abbie S. A. Chapman, Alexandre M. Chausson, Moses Chibesa, Joanne Davies, Emmanuel Dugan, Glory I. Edwards, Anthony Egeru, Tagel Gebrehiwot, Geoffrey H. Griffiths, Amleset Haile, Henry G. Hunga, Lizzy Igbine, Ousman M. Jarju, Francis Keya, Muhammad Khalifa, Wamba A. Ledoux, Lemlem T. Lejissa, Pius Loupa, Jonathan Lwanga, Everisto D. Mapedza, Robert Marchant, Tess McLoud, Patience Mukuyu, Labram M. Musah, Morton Mwanza, Jacob Mwitwa, Dora Neina, Tim Newbold, Samuel Njogo, Elizabeth J. Z. Robinson, Wales Singini, Bridget B. Umar, Frank Wesonga, Simon Willcock, Jingyi Yang, Joseph A. Tobias

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Evaluating stratospheric ozone and water vapour changes in CMIP6 models from 1850 to 2100 by J. Keeble, J. Keeble, B. Hassler, A. Banerjee, A. Banerjee, R. Checa-Garcia, G. Chiodo, G. Chiodo, S. Davis, V. Eyring, V. Eyring, P. T. Griffiths, P. T. Griffiths, O. Morgenstern, P. Nowack, P. Nowack, G. Zeng, J. Zhang, G. Bodeker, G. Bodeker, S. Burrows, P. Cameron-Smith, D. Cugnet, C. Danek, M. Deushi, L. W. Horowitz, A. Kubin, L. Li, G. Lohmann, M. Michou, M. J. Mills, P. Nabat, D. Olivié, S. Park, Ø. Seland, J. Stoll, K.-H. Wieners, T. Wu

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Reduced Complexity Model Intercomparison Project Phase 1: introduction and evaluation of global-mean temperature response by Z. R. J. Nicholls, Z. R. J. Nicholls, M. Meinshausen, M. Meinshausen, M. Meinshausen, J. Lewis, R. Gieseke, D. Dommenget, K. Dorheim, C.-S. Fan, J. S. Fuglestvedt, T. Gasser, U. Golüke, P. Goodwin, C. Hartin, A. P. Hope, E. Kriegler, N. J. Leach, D. Marchegiani, L. A. McBride, Y. Quilcaille, J. Rogelj, J. Rogelj, R. J. Salawitch, R. J. Salawitch, R. J. Salawitch, B. H. Samset, M. Sandstad, A. N. Shiklomanov, R. B. Skeie, C. J. Smith, C. J. Smith, S. Smith, K. Tanaka, K. Tanaka, J. Tsutsui, Z. Xie

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