Outcomes of Lensectomy in Hereditary Lens Subluxation by Mohammad-Hossein Dehghan, Reza Soleimanizad, Hamid Ahmadieh, Mohsen Azarmina, Masoud Soheilian, Siamak Moradian, Masoumeh Sanagoo

“…Underlying disorders leading to lens subluxation included Marfan syndrome (79.5%), Weill-Marchesani syndrome (8.2%), simple ectopia lentis (8.2%), and homocystinuria (4.1%). …”
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Dural ectasia by Neha Gupta, Veena Gupta, Abhishake Kumar, Gaurav Kumar

“…Its association with diseases like Marfans syndrome, neurofibromatosis, osteogenesis imperfecta, vertebral fracture, postopertative adhesions, trauma etc., is often overlooked as a reason for inadequate spinal anaesthesia. …”
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Modified pediatric Bentall procedure: A novel technique in a rare case by Gananjay G Salve, Satish R Javali, Bharat V Dalvi, Shivaprakash Krishnanaik

“…Only few cases with Marfans syndrome have been reported in the literature. …”
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17 β-Estradiol Impedes Aortic Root Dilation and Rupture in Male Marfan Mice by Louis Saddic, Sean Escopete, Lior Zilberberg, Shannon Kalsow, Divya Gupta, Mansoureh Eghbali, Sarah Parker

“…Marfan syndrome causes a hereditary form of thoracic aortic aneurysms with worse outcomes in male compared to female patients. …”
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Symptomatic unruptured pediatric intracranial aneurysm poses a diagnostic and management dilemma by Ali Hammed, Moufid Mahfoud, Salah Hammed

“…Results: Our case is a 10-year-old boy suddenly presented to the emergency department complained of severe headache, diplopia and partial ptosis.There was no history of systemic upset, trauma or relevant medical or surgical history.Urgent brain CT scan and Brain MRI were performed with normal findings.The patient was admitted to pediatric ICU for ICP monitoring.Standard clinical examination and laboratory investigations were done to exclude intracranial infection, toxins and metabolic conditions.Enhanced CT angiography revealed a 5 mm saccular ICA bifurcation aneurysm on the left side.Detailed screening and imaging were done to rule out any associated conditions, such as Autosomal dominant polycystic kidney disease (ADPKD), fibro muscular dysplasia, coarctation of aorta, Ehlers syndrome, and Marfans syndrome.A multi-disciplinary team (MDT) meeting had been held and surgery was recommended after interdisciplinary decision with radiologist and two neurosurgeons.The patient underwent microsurgical clip ligation of ICA bifurcation aneurysm after 10 days of symptoms. …”
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TRANSPOSITION OF GREAT ARTERIES: NEW INSIGHTS INTO THE PATHOGENESIS by Marta eUnolt, Carolina ePutotto, Lucia Martina Silvestri, Dario eMarino, Alessia eScarabotti, Valerio eMassaccesi, Angela eCaiaro, Paolo eVersacci, Bruno eMarino, Bruno eMarino

“…TGA is very rarely associated with the most frequent genetic syndromes, such as Turner, Noonan, Williams or Marfan syndromes, and in Down syndrome, it is virtually absent. …”
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