Combined overexpression of ATXN1L and mutant ATXN1 knockdown by AAV rescue motor phenotypes and gene signatures in SCA1 mice by Ellie M. Carrell, Megan S. Keiser, Ashley B. Robbins, Beverly L. Davidson

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RNAi or overexpression: Alternative therapies for Spinocerebellar Ataxia Type 1 by Megan S. Keiser, James C. Geoghegan, Ryan L. Boudreau, Kim A. Lennox, Beverly L. Davidson

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Ataxin-1 oligomers induce local spread of pathology and decreasing them by passive immunization slows Spinocerebellar ataxia type 1 phenotypes by Cristian A Lasagna-Reeves, Maxime WC Rousseaux, Marcos J Guerrero-Munoz, Luis Vilanova-Velez, Jeehye Park, Lauren See, Paymaan Jafar-Nejad, Ronald Richman, Harry T Orr, Rakez Kayed, Huda Y Zoghbi

Subjects: “…ataxin-1…”
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Twenty-five years since the identification of the first SCA gene: history, clinical features and perspectives for SCA1 by Carlos Roberto Martins Junior, Fabrício Castro de Borba, Alberto Rolim Muro Martinez, Thiago Junqueira Ribeiro de Rezende, Iscia Lopes Cendes, José Luiz Pedroso, Orlando Graziani Povoas Barsottini, Marcondes Cavalcante França Júnior

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A native interactor scaffolds and stabilizes toxic ATAXIN-1 oligomers in SCA1 by Cristian A Lasagna-Reeves, Maxime WC Rousseaux, Marcos J Guerrero-Muñoz, Jeehye Park, Paymaan Jafar-Nejad, Ronald Richman, Nan Lu, Urmi Sengupta, Alexandra Litvinchuk, Harry T Orr, Rakez Kayed, Huda Y Zoghbi

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Mechanisms of tunneling nanotube-based propagation of neurodegenerative disease proteins by Sarita Lagalwar

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The novel multiple sclerosis susceptibility gene ATXN1 regulates B cell receptor signaling in B-1a cells by Qin Ma, Alessandro Didonna

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On the identification of potential novel therapeutic targets for spinocerebellar ataxia type 1 (SCA1) neurodegenerative disease using EvoPPI3 by Sousa André, Rocha Sara, Vieira Jorge, Reboiro-Jato Miguel, López-Fernández Hugo, Vieira Cristina P.

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Enhanced Age-Dependent Motor Impairment in Males of <i>Drosophila melanogaster</i> Modeling Spinocerebellar Ataxia Type 1 Is Linked to Dysregulation of a Matrix Metalloproteinase by Emma M. Palmer, Caleb A. Snoddy, Peyton M. York, Sydney M. Davis, Madelyn F. Hunter, Natraj Krishnan

Subjects: “…ataxin1…”
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Modest Reduction in CAG Repeat Length Rescues Motor Deficits but Not Purkinje Cell Pathology and Gliosis in Spinocerebellar Ataxia Type 1 Mice by Stephen Gilliat, Juao-Guilherme Rosa, Genevieve Benjamin, Kaelin Sbrocco, Wensheng Lin, Marija Cvetanovic

Subjects: “…ATAXIN-1…”
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Brain Derived Neurotrophic Factor (BDNF) Delays Onset of Pathogenesis in Transgenic Mouse Model of Spinocerebellar Ataxia Type 1 (SCA1) by Aaron Mellesmoen, Carrie Sheeler, Austin Ferro, Orion Rainwater, Marija Cvetanovic, Marija Cvetanovic

Subjects: “…ATAXIN-1…”
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Altered Purkinje cell miRNA expression and SCA1 pathogenesis by Edgardo Rodriguez-Lebron, Gumei Liu, Megan Keiser, Mark A. Behlke, Beverly L. Davidson

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Inhibition of colony-stimulating factor 1 receptor early in disease ameliorates motor deficits in SCA1 mice by Wenhui Qu, Andrea Johnson, Joo Hyun Kim, Abigail Lukowicz, Daniel Svedberg, Marija Cvetanovic

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Gene, Stem Cell, and Alternative Therapies for SCA 1 by Jacob Lewis Wagner, Deirdre Margaret O'Connor, Anthony Donsante, Nicholaus M Boulis

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Identification of the ataxin-1 interaction network and its impact on spinocerebellar ataxia type 1 by Jiu-Ming Chen, Shi-Kai Chen, Pei-Pei Jin, Shun-Chang Sun

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Intranuclear inclusions of polyQ-expanded ATXN1 sequester RNA molecules by Ioannis Gkekas, Ioannis Gkekas, Aimilia-Christina Vagiona, Nikolaos Pechlivanis, Georgia Kastrinaki, Katerina Pliatsika, Katerina Pliatsika, Sebastian Iben, Konstantinos Xanthopoulos, Konstantinos Xanthopoulos, Fotis E. Psomopoulos, Miguel A. Andrade-Navarro, Spyros Petrakis

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5′UTR-mediated regulation of Ataxin-1 expression by Rachna Manek, Tiffany Nelson, Elizabeth Tseng, Edgardo Rodriguez-Lebron

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Generation of induced pluripotent stem cell(iPSC)line CJUHi001-A derived peripheral blood mononuclear cells of spinocerebellar ataxia type 1(SCA1) the CAG repeat mutation in ATXN1... by Yinshi Jin, Guangxian Nan

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