Differential regulation of progranulin derived granulin peptides by Tingting Zhang, Huan Du, Mariela Nunez Santos, Xiaochun Wu, Mitchell D. Pagan, Lianne Jillian Trigiani, Nozomi Nishimura, Thomas Reinheckel, Fenghua Hu

Subjects: “…Frontotemporal lobar degeneration (FTLD)…”
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Feasibility and acceptability of remote smartphone cognitive testing in frontotemporal dementia research by Jack Carson Taylor, Hilary W. Heuer, Annie L. Clark, Amy B. Wise, Masood Manoochehri, Leah Forsberg, Carly Mester, Meghana Rao, Daniell Brushaber, Joel Kramer, Ariane E. Welch, John Kornak, Walter Kremers, Brian Appleby, Bradford C. Dickerson, Kimiko Domoto‐Reilly, Julie A. Fields, Nupur Ghoshal, Neill Graff‐Radford, Murray Grossman, Matthew GH Hall, Edward D. Huey, David Irwin, Maria I. Lapid, Irene Litvan, Ian R. Mackenzie, Joseph C. Masdeu, Mario F. Mendez, Naomi Nevler, Chiadi U. Onyike, Belen Pascual, Peter Pressman, Katherine P. Rankin, Buddhika Ratnasiri, Julio C. Rojas, Maria Carmela Tartaglia, Bonnie Wong, Maria Luisa Gorno‐Tempini, Bradley F. Boeve, Howard J. Rosen, Adam L. Boxer, Adam M. Staffaroni

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Increase in wasteosomes (corpora amylacea) in frontotemporal lobar degeneration with specific detection of tau, TDP-43 and FUS pathology by Raquel Alsina, Marta Riba, Agnès Pérez-Millan, Sergi Borrego-Écija, Iban Aldecoa, Clara Romera, Mircea Balasa, Anna Antonell, Albert Lladó, Yaroslau Compta, Jaume del Valle, Raquel Sánchez-Valle, Carme Pelegrí, Laura Molina-Porcel, Jordi Vilaplana

Subjects: “…Frontotemporal lobar degeneration (FTLD)…”
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Editorial: The role of gene mutations in the neuropathology of amyotrophic lateral sclerosis (ALS) and frontotemporal lobar degeneration (FTLD)– Progress and challenges by Claire Troakes, Francesca Luisa Conforti

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Frontotemporal dementia-like disease progression elicited by seeded aggregation and spread of FUS by Sonia Vazquez-Sanchez, Britt Tilkin, Fatima Gasset-Rosa, Sitao Zhang, Diana Piol, Melissa McAlonis-Downes, Jonathan Artates, Noe Govea-Perez, Yana Verresen, Lin Guo, Don W. Cleveland, James Shorter, Sandrine Da Cruz

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Distinct molecular patterns of TDP-43 pathology in Alzheimer’s disease: relationship with clinical phenotypes by Sandra O. Tomé, Rik Vandenberghe, Simona Ospitalieri, Evelien Van Schoor, Thomas Tousseyn, Markus Otto, Christine A. F. von Arnim, Dietmar Rudolf Thal

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Editorial: Horizon in frontotemporal lobar degeneration related disorder by Qianqian He, Min Chu, Liyong Wu

Subjects: “…frontotemporal lobar degeneration (FTLD)…”
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Populations of Tau Conformers Drive Prion-like Strain Effects in Alzheimer’s Disease and Related Dementias by Lenka Hromadkova, Mohammad Khursheed Siddiqi, He Liu, Jiri G. Safar

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The Pathobiology of TDP-43 C-Terminal Fragments in ALS and FTLD by Britt A. Berning, Adam K. Walker, Adam K. Walker

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Human Induced Pluripotent Stem Cell Models of Frontotemporal Dementia With Tau Pathology by Rebekka Kühn, Aayushi Mahajan, Peter Canoll, Gunnar Hargus, Gunnar Hargus

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Case Report: Semantic Variant of Primary Progressive Aphasia Associated With Anti-Glial Fibrillary Acid Protein Autoantibodies by Niels Hansen, Winfried Stöcker, Jens Wiltfang, Jens Wiltfang, Jens Wiltfang, Claudia Bartels, Kristin Rentzsch, Caroline Bouter

Subjects: “…frontotemporal lobar degeneration (FTLD)…”
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Tweaking Progranulin Expression: Therapeutic Avenues and Opportunities by Joke Terryn, Joke Terryn, Catherine M. Verfaillie, Philip Van Damme, Philip Van Damme, Philip Van Damme

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Molecular Mechanisms of TDP-43 Misfolding and Pathology in Amyotrophic Lateral Sclerosis by Archana Prasad, Vidhya Bharathi, Vishwanath Sivalingam, Amandeep Girdhar, Basant K. Patel

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Lysosome dysfunction as a cause of neurodegenerative diseases: Lessons from frontotemporal dementia and amyotrophic lateral sclerosis by Jessica Root, Paola Merino, Austin Nuckols, Michelle Johnson, Thomas Kukar

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New Antibody-Free Mass Spectrometry-Based Quantification Reveals That C9ORF72 Long Protein Isoform Is Reduced in the Frontal Cortex of Hexanucleotide-Repeat Expansion Carriers by Arthur Viodé, Clémence Fournier, Clémence Fournier, Agnès Camuzat, Agnès Camuzat, François Fenaille, NeuroCEB Brain Bank, Morwena Latouche, Morwena Latouche, Fanny Elahi, Isabelle Le Ber, Isabelle Le Ber, Isabelle Le Ber, Christophe Junot, Foudil Lamari, Foudil Lamari, Vincent Anquetil, Vincent Anquetil, François Becher, Franck Letournel, Anne Vital, Françoise Chapon, Catherine Godfraind, Claude-Alain Maurage, Vincent Deramecourt, David Meyronnet, Nathalie Streichenberger, André Maues de Paula, Valérie Rigau, Fanny Vandenbos-Burel, Charles Duyckaerts, Danielle Seilhean, Véronique Sazdovitch, Serge Milin, Dan Christian Chiforeanu, Annie Laquerrière, Béatrice Lannes

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A phase 1b open‐label study of sodium selenate as a disease‐modifying treatment for possible behavioral variant frontotemporal dementia by Lucy Vivash, Charles B. Malpas, Christian Meletis, Meghan Gollant, Dhamidhu Eratne, Qiao‐Xin Li, Stuart McDonald, William T. O'Brien, Amy Brodtmann, David Darby, Christopher Kyndt, Mark Walterfang, Christopher M. Hovens, Dennis Velakoulis, Terence J. O'Brien

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Increased metal content in the TDP-43A315T transgenic mouse model of frontotemporal lobar degeneration and amyotrophic lateral sclerosis by Theresa eDang, Nastasia eLim, Alexandra eGrubman, Qiao-Xin eLi, Irene eVolitakis, Anthony Robert White, Peter eCrouch

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Lipopolysaccharide triggers exacerbated microglial activation, excessive cytokine release and behavioural disturbances in mice with truncated Fused-in-Sarcoma Protein (FUS) by Alexander Trofimov, Dmitrii Pavlov, Anand Goswami, Anna Gorlova, Kirill Chaprov, Aleksei Umriukhin, Allan Kalueff, Alexey Deykin, Klaus-Peter Lesch, Daniel Clive Anthony, Tatyana Strekalova

Subjects: “…Frontotemporal lobar degeneration (FTLD)…”
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Neurodegenerative Disease-Associated TDP-43 Fragments Are Extracellularly Secreted with CASA Complex Proteins by Elena Casarotto, Daisy Sproviero, Eleonora Corridori, Maria Cristina Gagliani, Marta Cozzi, Marta Chierichetti, Riccardo Cristofani, Veronica Ferrari, Mariarita Galbiati, Francesco Mina, Margherita Piccolella, Paola Rusmini, Barbara Tedesco, Stella Gagliardi, Katia Cortese, Cristina Cereda, Angelo Poletti, Valeria Crippa

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