Structural Transition, Function and Dysfunction of TDP-43 in Neurodegenerative Diseases by Tariq Afroz, Manuela Pérez-Berlanga, Magdalini Polymenidou

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Membrane Interactions and Toxicity by Misfolded Protein Oligomers by Mario Gonzalez-Garcia, Giuliana Fusco, Alfonso De Simone, Alfonso De Simone

Subjects: “…protein misfolding…”
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Comparative Transcriptomic Analysis Reveals Adaptive Traits in Antarctic Scallop <i>Adamussium colbecki</i> by Samuele Greco, Giacomo Voltarel, Anastasia Serena Gaetano, Chiara Manfrin, Alberto Pallavicini, Piero Giulio Giulianini, Marco Gerdol

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Transthyretin Stabilization: An Emerging Strategy for the Treatment of Alzheimer’s Disease? by Federica Saponaro, Jin Hae Kim, Grazia Chiellini

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HspB5 Chaperone Structure and Activity Are Modulated by Chemical-Scale Interactions in the ACD Dimer Interface by Chenwei Wang, Lilong Teng, Zhiyan Silvia Liu, Aichurok Kamalova, Kathryn A. McMenimen

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Mitochondria and endoplasmic reticulum crosstalk in amyotrophic lateral sclerosis by Giovanni Manfredi, Hibiki Kawamata

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The Mechanism of Mitochondrial Injury in Alpha-1 Antitrypsin Deficiency Mediated Liver Disease by Nazli Khodayari, Rejean L. Wang, Regina Oshins, Yuanqing Lu, Michael Millett, Alek M. Aranyos, Sayedamin Mostofizadeh, Yogesh Scindia, Tammy O. Flagg, Mark Brantly

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Skd3 (human ClpB) is a potent mitochondrial protein disaggregase that is inactivated by 3-methylglutaconic aciduria-linked mutations by Ryan R Cupo, James Shorter

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Polymorphism of amyloid-like fibrils can be defined by the concentration of seeds by Tomas Sneideris, Katažyna Milto, Vytautas Smirnovas

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Dissecting the Molecular Features of Systemic Light Chain (AL) Amyloidosis: Contributions from Proteomics by Paola Rognoni, Giulia Mazzini, Serena Caminito, Giovanni Palladini, Francesca Lavatelli

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The Cytotoxicity and Clearance of Mutant Huntingtin and Other Misfolded Proteins by Austin Folger, Yanchang Wang

Subjects: “…protein misfolding…”
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Hydration of Simple Model Peptides in Aqueous Osmolyte Solutions by Aneta Panuszko, Maciej Pieloszczyk, Anna Kuffel, Karol Jacek, Karol A. Biernacki, Sebastian Demkowicz, Janusz Stangret, Piotr Bruździak

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Zinc shapes the folding landscape of p53 and establishes a pathway for reactivating structurally diverse cancer mutants by Adam R Blanden, Xin Yu, Alan J Blayney, Christopher Demas, Jeung-Hoi Ha, Yue Liu, Tracy Withers, Darren R Carpizo, Stewart N Loh

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The effect of the chemical chaperone 4-phenylbutyrate on secretion and activity of the p.Q160R missense variant of coagulation factor FVII by Elisabeth Andersen, Maria Eugenia Chollet, Marcello Baroni, Mirko Pinotti, Francesco Bernardi, Ellen Skarpen, Per Morten Sandset, Grethe Skretting

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Safety and pharmacodynamic effects of a pharmacological chaperone on α-galactosidase A activity and globotriaosylceramide clearance in Fabry disease: report from two phase 2 clinic... by Germain Dominique P, Giugliani Roberto, Hughes Derralynn A, Mehta Atul, Nicholls Kathy, Barisoni Laura, Jennette Charles J, Bragat Alexander, Castelli Jeff, Sitaraman Sheela, Lockhart David J, Boudes Pol F

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Generating Ensembles of Dynamic Misfolding Proteins by Theodoros K. Karamanos, Arnout P. Kalverda, Sheena E. Radford

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Nuclear export of misfolded SOD1 mediated by a normally buried NES-like sequence reduces proteotoxicity in the nucleus by Yongwang Zhong, Jiou Wang, Mark J Henderson, Peixin Yang, Brian M Hagen, Teepu Siddique, Bruce E Vogel, Han-Xiang Deng, Shengyun Fang

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Amyloid Disassembly: What Can We Learn from Chaperones? by Zaida L. Almeida, Rui M. M. Brito

Subjects: “…protein misfolding…”
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Prion Diseases: A Unique Transmissible Agent or a Model for Neurodegenerative Diseases? by Diane L. Ritchie, Marcelo A. Barria

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From the Light Chain Sequence to the Tissue Microenvironment: Contribution of the Mesangial Cells to Glomerular Amyloidosis by Luis Del Pozo-Yauner, Elba A. Turbat-Herrera, Julio I. Pérez-Carreón, Guillermo A. Herrera

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