Retained primary teeth in STAT3 hyper-IgE syndrome: early intervention in childhood is essential

Retained primary teeth in STAT3 hyper-IgE syndrome: early intervention in childhood is essential

Abstract Background STAT3 hyper-IgE syndrome (STAT3-HIES) is a rare primary immunodeficiency that clinically overlaps with atopic dermatitis. In addition to eczema, elevated serum-IgE, and recurrent infections, STAT3-HIES patients suffer from characteristic facies, midline defects, and retained prim...

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Bibliographic Details
Main Authors: Iris Meixner, Beate Hagl, Carolin I. Kröner, Benedikt D. Spielberger, Ekaterini Paschos, Gregor Dückers, Tim Niehues, Ronny Hesse, Ellen D. Renner
Format: Article
Language:English
Published: BMC 2020-09-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Retained primary teeth
Delayed eruption of permanent teeth
Root resorption
Hyper-IgE syndrome
HIES
STAT3
Online Access:http://link.springer.com/article/10.1186/s13023-020-01516-3

Internet

http://link.springer.com/article/10.1186/s13023-020-01516-3

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