Insights into lipid accumulation in skeletal muscle in dysferlin-deficient mice

Loss of dysferlin (DYSF) protein in humans results in limb-girdle muscular dystrophy 2B, characterized by progressive loss of muscles in the distal limbs with impaired locomotion. The DYSF-null (Bla/J) mouse develops severe steatotic muscles upon aging. Here, we report a marked increase in adipocyte...

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Détails bibliographiques
Auteurs principaux: Anil K. Agarwal, Katie Tunison, Matthew A. Mitsche, Jeffrey G. McDonald, Abhimanyu Garg
Format: Article
Langue:English
Publié: Elsevier 2019-12-01
Collection:Journal of Lipid Research
Sujets:
Accès en ligne:http://www.sciencedirect.com/science/article/pii/S0022227520310440