Severe dyspnea in a patient with neurofibromatosis type 1
Neurofibromatosis type 1 (NF1) is a genetic disease in which pulmonary complications are rare, but severe, especially pulmonary hypertension (PH). The mechanisms underlying the onset of PH in patients with NF1 are unclear and might be multifactorial. In particular, the frequent presence of pulmonary...
Main Authors: | , , |
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Format: | Article |
Language: | English |
Published: |
Elsevier
2017-01-01
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Series: | Respiratory Medicine Case Reports |
Online Access: | http://www.sciencedirect.com/science/article/pii/S2213007117301831 |