Airway Findings in Patients with Hunter Syndrome Treated with Intravenous Idursulfase

Airway Findings in Patients with Hunter Syndrome Treated with Intravenous Idursulfase

People with Hunter syndrome are known to be affected by a variety of airway pathologies. Treatment of Hunter syndrome with the enzyme replacement therapy (ERT) idursulfase is now the standard of care. However, it is not known how ERT changes the progression of airway involvement. To evaluate this, w...

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Bibliographic Details
Main Authors: Richard De Vuyst, Elizabeth Jalazo, Tamy Moraes Tsujimoto, Feng-Chang Lin, Joseph Muenzer, Marianne S. Muhlebach
Format: Article
Language:English
Published: MDPI AG 2023-01-01
Series:Journal of Clinical Medicine
Subjects:
tracheopathy
Hunter syndrome
lysosomal storage disease
bronchoscopy
airway severity score
enzyme replacement therapy
Online Access:https://www.mdpi.com/2077-0383/12/2/480

Internet

https://www.mdpi.com/2077-0383/12/2/480

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