Small airways morphological alterations associated with functional impairment in lymphangioleiomyomatosis

Small airways morphological alterations associated with functional impairment in lymphangioleiomyomatosis

Abstract Background Lymphangioleiomyomatosis (LAM) is a rare neoplastic and cystic pulmonary disease characterized by abnormal proliferation of the so-called LAM cells. Despite the functional obstructive pattern observed in most patients, few studies investigated the morphological changes in the sma...

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Bibliographic Details
Main Authors: Lígia Pelosi Mendonça, Natalia de Souza Xavier Costa, Ellen Caroline Toledo do Nascimento, Martina Rodrigues de Oliveira, Carlos Roberto Ribeiro de Carvalho, Bruno Guedes Baldi, Marisa Dolhnikoff
Format: Article
Language:English
Published: BMC 2024-01-01
Series:BMC Pulmonary Medicine
Subjects:
Lymphangioleiomyomatosis
Small airways
Pulmonary function test
LAM Score
Immunohistochemistry
Online Access:https://doi.org/10.1186/s12890-023-02837-2

Internet

https://doi.org/10.1186/s12890-023-02837-2

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