Case Report: Dexmedetomidine for Intractable Clusters of Myoclonic Jerks and Paroxysmal Sympathetic Hyperactivity in Progressive Encephalomyelitis With Rigidity and Myoclonus

Case Report: Dexmedetomidine for Intractable Clusters of Myoclonic Jerks and Paroxysmal Sympathetic Hyperactivity in Progressive Encephalomyelitis With Rigidity and Myoclonus

Introduction: Progressive encephalomyelitis with rigidity and myoclonus (PERM) is a severe form of stiff-person spectrum disorder characterized by painful spasms, myoclonic jerks, hyperekplexia, brainstem dysfunction, and dysautonomia, which is sometimes resistant to γ-amino-butyric acid (GABA)-ergi...

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Váldodahkkit: Yuzo Fujino, Kensuke Shiga, Masatoshi Hori, Aiko Tamura, Takahiro Iizuka
Materiálatiipa: Artihkal
Giella:English
Almmustuhtton: Frontiers Media S.A. 2021-07-01
Ráidu:Frontiers in Neurology
Fáttát:
α2-adrenergic receptor
dexmedetomidine
glycine receptor
myoclonus
paroxysmal sympathetic hyperactivity
stiff–person syndrome
Liŋkkat:https://www.frontiersin.org/articles/10.3389/fneur.2021.703050/full

Interneahtta

https://www.frontiersin.org/articles/10.3389/fneur.2021.703050/full

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