Complete Remission in a TEMPI Syndrome Treated with a Daratumumab, Lenalidomide, and Dexamethasone-Based Regimen: A Case Report

Introduction: TEMPI syndrome is a rare and acquired condition which is characterized by five classical features: telangiectasias, erythrocytosis with elevated erythropoietin, monoclonal gammopathy, perinephric fluid collections, and intrapulmonary shunting. The classical treatment is based on bortez...

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Bibliographic Details
Main Authors: Pierre-Yves Sansen, Luc Montfort, Anne Nanquette, Julien Depaus, Hélène Vellemans
Format: Article
Language:English
Published: Karger Publishers 2024-01-01
Series:Case Reports in Oncology
Subjects:
Online Access:https://beta.karger.com/Article/FullText/535551