Immune‐Mediated Myocarditis in Fabry Disease Cardiomyopathy

Background Glycosphingolipid accumulation in Fabry cells generates a proinflammatory response that may influence disease evolution and responsiveness to enzyme replacement therapy. This study evaluated incidence, mechanism, and impact of myocarditis in Fabry disease cardiomyopathy (FDCM). Methods an...

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Bibliographic Details
Main Authors: Andrea Frustaci, Romina Verardo, Claudia Grande, Nicola Galea, Pierluca Piselli, Iacopo Carbone, Maria Alfarano, Matteo Antonio Russo, Cristina Chimenti
Format: Article
Language:English
Published: Wiley 2018-09-01
Series:Journal of the American Heart Association: Cardiovascular and Cerebrovascular Disease
Subjects:
Online Access:https://www.ahajournals.org/doi/10.1161/JAHA.118.009052