Identification of the Occipito-Pontine Tract Using Diffusion-Tensor Fiber Tracking in Adult-Onset Adrenoleukodystrophy with Topographic Disorientation

X-linked adrenoleukodystrophy is a severe and progressive neurodegenerative disease caused by the peroxisomal transporter ATP-binding cassette, subfamily D, member 1 gene mutations. The defect of this gene product results in accumulation of very-long-chain fatty acids in organs and serum, central de...

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Bibliographic Details
Main Authors: Yuji Uchida, En Kimura, Teruyuki Hirano, Shinsuke Nishi, Yasushi Maeda, Satoshi Yamashita, Keiko Ueno-Shuto, Naofumi Tokutomi, Mika Kitajima, Toshinori Hirai, Makoto Uchino
Format: Article
Language:English
Published: Karger Publishers 2011-05-01
Series:Case Reports in Neurology
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Online Access:http://www.karger.com/Article/FullText/328962