Natural history of respiratory muscle strength in spinal muscular atrophy: a prospective national cohort study

Natural history of respiratory muscle strength in spinal muscular atrophy: a prospective national cohort study

Abstract Background Respiratory complications are the most important cause of morbidity and mortality in spinal muscular atrophy (SMA). Respiratory muscle weakness results in impaired cough, recurrent respiratory tract infections and eventually can cause respiratory failure. We assessed longitudinal...

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Bibliographic Details
Main Authors: Esther S. Veldhoen, Camiel A. Wijngaarde, Erik H. J. Hulzebos, Roelie M. Wösten-van Asperen, Renske I. Wadman, Ruben P. A. van Eijk, Fay Lynn Asselman, Marloes Stam, Louise A. M. Otto, Inge Cuppen, Feline E. V. Scheijmans, Laura P. Verweij-van den Oudenrijn, Bart Bartels, Michael A. Gaytant, Cornelis K. van der Ent, W. Ludo van der Pol
Format: Article
Language:English
Published: BMC 2022-02-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Neuromuscular
Spinal muscular atrophy
Respiratory muscle strength
Lung function
Natural history
Online Access:https://doi.org/10.1186/s13023-022-02227-7

Internet

https://doi.org/10.1186/s13023-022-02227-7

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